Kimura Akihisa, Tsuji Masaki, Isogai Toshiaki, Nagata Kenichiro, Kato Ken, Hisagi Motoyuki, Nonaka Takahiro, Ninomiya Mikio, Kiriu Takahiro, Tanaka Hiroyuki, Tejima Tamotsu
Department of Cardiology, Tokyo Metropolitan Tama Medical Center, Japan.
Department of Cardiovascular Surgery, Tokyo Metropolitan Tama Medical Center, Japan.
Intern Med. 2018 Dec 15;57(24):3575-3580. doi: 10.2169/internalmedicine.0657-17. Epub 2018 Aug 10.
A 43-year-old woman presented with worsening shortness of breath and lower-extremity edema. Echocardiography and computed tomography showed obstruction of blood flow due to a mass filling the right atrium. Emergency surgery was performed for circulatory failure. Primary cardiac rhabdomyosarcoma was diagnosed based on a histological examination. The patient died about two months after the diagnosis despite surgical excision and radiation therapy. The poor prognosis may have resulted from the grossly incomplete removal of the tumor and chemotherapy intolerance. We herein report a case of primary cardiac rhabdomyosarcoma filling the right atrium and offer possible reasons for the poor prognosis.
一名43岁女性因呼吸急促和下肢水肿加重前来就诊。超声心动图和计算机断层扫描显示,右心房被一个肿块占据,导致血流受阻。因循环衰竭进行了急诊手术。根据组织学检查诊断为原发性心脏横纹肌肉瘤。尽管进行了手术切除和放射治疗,但患者在诊断后约两个月死亡。预后不良可能是由于肿瘤切除极不完全以及对化疗不耐受所致。我们在此报告一例右心房被原发性心脏横纹肌肉瘤占据的病例,并探讨预后不良的可能原因。