Thankamony Priyakumari, Chandar Rumesh, Kattoor Jayasree, Nair Ramachandran Krishnankutty
Department of Pediatric Oncology, Regional Cancer Centre, Trivandrum, Kerala, India.
Department of Pediatric Oncology, Regional Cancer Centre, Trivandrum, Kerala, India.
J Pediatr Adolesc Gynecol. 2018 Dec;31(6):629-631. doi: 10.1016/j.jpag.2018.08.008. Epub 2018 Sep 1.
Angiosarcoma is an uncommon high-grade sarcoma in children. Visceral angiosarcoma involving the ovary is extremely rare. Because of the lack of recurrent cytogenetic alterations, histopathological identification of this uncommon tumor in unusual sites like the ovary demands pathologic expertise. Complete surgical resection and radiotherapy are the chief treatment modalities determining survival, with chemotherapy contributing a minor role.
We discuss a 11-year-old prepubertal girl who presented with primary angiosarcoma of the ovary.
Early realization of such exceptional presentations of these tumors is needed to achieve the best treatment outcome.
血管肉瘤是儿童中一种罕见的高级别肉瘤。累及卵巢的内脏血管肉瘤极为罕见。由于缺乏复发性细胞遗传学改变，在卵巢等不寻常部位对这种罕见肿瘤进行组织病理学鉴定需要病理专业知识。完整的手术切除和放疗是决定生存的主要治疗方式，化疗起次要作用。
我们讨论一名11岁青春期前女孩，她患有原发性卵巢血管肉瘤。
需要尽早认识到这些肿瘤的此类特殊表现，以实现最佳治疗效果。
