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穿透性胎盘植入合并子宫破裂和血栓性微血管病。

Placenta percreta complicated by uterine rupture and thrombotic microangiopathy.

作者信息

Laužikienė Dalia, Vosylius Saulius, Šiaudinytė Ieva, Laužikas Emilis, Ramašauskaitė Diana, Bartkevičienė Daiva

机构信息

Department of Obstetrics and Gynaecology, Faculty of Medicine, Vilnius University, Vilnius, Lithuania.

Clinic of Anaesthesiology and Intensive Care, Faculty of Medicine, Vilnius University Vilnius, Lithuania.

出版信息

Acta Med Litu. 2018;25(2):61-65. doi: 10.6001/actamedica.v25i2.3758.

DOI:10.6001/actamedica.v25i2.3758
PMID:30210239
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC6130928/
Abstract

BACKGROUND

Uterine rupture at the site of a previous caesarean scar with abnormal placental penetration through the uterus wall with bladder invasion is a rare and serious pregnancy complication. Our aim was to report a case of uterine rupture with placenta percreta complicated by thrombotic microangiopathy.

MATERIALS AND METHODS

We did a literature review and analysed medical documentation retrospectively.

RESULTS

A patient was admitted with complaints of lower abdominal pain at 21 weeks of gestation. Sonography of the caesarean scar increased suspicion of placental penetration. Anaemia, thrombocytopenia, coagulopathy, and acute kidney injury developed and led to the diagnosis of thrombotic microangiopathy. The termination of pregnancy was required due to severe deterioration in organ functions. The complete uterine rupture with placenta percreta invading the urinary bladder was confirmed, and total hysterectomy was performed to control life-threatening haemorrhage. The patient was treated by blood component transfusions, renal replacement therapy, and plasmapheresis. Good health was confirmed two months later by laboratory and instrumental tests.

CONCLUSIONS

It is a rare but very serious condition that increases morbidity of mother and foetus, therefore immediate diagnostics and treatment are required.

摘要

背景

既往剖宫产瘢痕部位子宫破裂,胎盘异常穿透子宫壁并侵犯膀胱,是一种罕见且严重的妊娠并发症。我们的目的是报告一例子宫破裂合并胎盘植入并发血栓性微血管病的病例。

材料与方法

我们进行了文献综述并回顾性分析了医疗记录。

结果

一名患者在妊娠21周时因下腹部疼痛入院。剖宫产瘢痕的超声检查增加了胎盘穿透的怀疑。出现贫血、血小板减少、凝血病和急性肾损伤,导致血栓性微血管病的诊断。由于器官功能严重恶化,需要终止妊娠。证实为完全性子宫破裂,胎盘植入侵犯膀胱,行全子宫切除术以控制危及生命的出血。患者接受了成分输血、肾脏替代治疗和血浆置换治疗。两个月后通过实验室和仪器检查确认健康状况良好。

结论

这是一种罕见但非常严重的情况,会增加母婴发病率,因此需要立即进行诊断和治疗。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2d01/6130928/a4f07594902d/aml-25-061-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2d01/6130928/428480d3ca50/aml-25-061-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2d01/6130928/a4f07594902d/aml-25-061-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2d01/6130928/428480d3ca50/aml-25-061-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2d01/6130928/a4f07594902d/aml-25-061-g002.jpg

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本文引用的文献

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Am J Obstet Gynecol. 2017 May;216(5):510.e1-510.e6. doi: 10.1016/j.ajog.2017.01.019. Epub 2017 Jan 20.
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Pregnancy-related thrombotic microangiopathies: Clues from complement biology.妊娠相关血栓性微血管病:补体生物学的线索
Transfus Apher Sci. 2016 Apr;54(2):199-202. doi: 10.1016/j.transci.2016.04.009. Epub 2016 Apr 25.
3
Escalating placenta invasiveness: repeated placenta accreta at the limit of viability.
胎盘侵袭性增加:在存活极限时反复发生胎盘植入。
Int J Womens Health. 2016 Apr 15;8:119-23. doi: 10.2147/IJWH.S100321. eCollection 2016.
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Pregnancy-Associated Atypical Hemolytic-Uremic Syndrome.妊娠相关非典型溶血尿毒综合征
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Placenta Percreta With Invasion into the Urinary Bladder.胎盘植入伴侵犯膀胱
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Disseminated intravascular coagulation in pregnancy: insights in pathophysiology, diagnosis and management.妊娠期弥散性血管内凝血:病理生理学、诊断与管理的见解
Am J Obstet Gynecol. 2015 Oct;213(4):452-63. doi: 10.1016/j.ajog.2015.03.054. Epub 2015 Mar 31.
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Diagnosis and management of placenta percreta with bladder involvement.合并膀胱受累的穿透性胎盘植入的诊断与处理
J Obstet Gynaecol. 2015 Apr;35(3):308-10. doi: 10.3109/01443615.2014.949226. Epub 2014 Aug 25.
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Hemolytic uremic syndrome.溶血尿毒综合征
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