Department of Oculoplasty, Sri Sankaradeva Nethralaya, Guwahati, Assam, India.
Department of Ophthalmology, Sri Sankaradeva Nethralaya, Guwahati, Assam, India.
Indian J Ophthalmol. 2018 Oct;66(10):1508-1511. doi: 10.4103/ijo.IJO_316_18.
Hypereosinophilic syndrome (HES) is a spectrum of myeloproliferative disorder, which is characterized by persistent and marked blood eosinophilia and damage to multiple organs due to eosinophilic infiltration. Idiopathic HES is identified after ruling out all other causes of eosinophilia. Poor prognosis is usually associated with cardiac involvement and malignant transformation of blood cells. We report a rare case of HES in an 8-year-old boy who presented with unilateral proptosis and torticollis. The patient responded well to corticosteroid therapy with reduction of proptosis and torticollis and normalization of serum eosinophil count.
高嗜酸性粒细胞综合征(HES)是一组骨髓增殖性疾病,其特征是持续性和显著的血液嗜酸性粒细胞增多,并因嗜酸性粒细胞浸润而导致多个器官受损。特发性 HES 是在排除所有其他嗜酸性粒细胞增多的原因后确定的。预后不良通常与心脏受累和血细胞恶性转化有关。我们报告了一例罕见的 8 岁男孩 HES 病例,该患者表现为单侧眼球突出和斜颈。患者对皮质类固醇治疗反应良好,眼球突出和斜颈减轻,血清嗜酸性粒细胞计数恢复正常。