Department of Medicine, Albert Einstein College of Medicine, Bronx, New York.
Department of Nutrition and Metabolism, University of Texas Medical Branch , Galveston, Texas.
Am J Physiol Renal Physiol. 2018 Dec 1;315(6):F1658-F1669. doi: 10.1152/ajprenal.00314.2018. Epub 2018 Oct 3.
Muscle dysfunction is an important cause of morbidity among patients with chronic kidney disease (CKD). Although muscle fibrosis is present in a CKD rodent model, its existence in humans and its impact on physical function are currently unknown. We examined isometric leg extension strength and measures of skeletal muscle fibrosis and inflammation in vastus lateralis muscle from CKD patients ( n = 10) and healthy, sedentary controls ( n = 10). Histochemistry and immunohistochemistry were used to assess muscle collagen and macrophage and fibro/adipogenic progenitor (FAP) cell populations, and RT-qPCR was used to assess muscle-specific inflammatory marker expression. Muscle collagen content was significantly greater in CKD compared with control (18.8 ± 2.1 vs. 11.7 ± 0.7% collagen area, P = 0.008), as was staining for collagen I, pro-collagen I, and a novel collagen-hybridizing peptide that binds remodeling collagen. Muscle collagen was inversely associated with leg extension strength in CKD ( r = -0.74, P = 0.01). FAP abundance was increased in CKD, was highly correlated with muscle collagen ( r = 0.84, P < 0.001), and was inversely associated with TNF-α expression ( r = -0.65, P = 0.003). TNF-α, CD68, CCL2, and CCL5 mRNA were significantly lower in CKD than control, despite higher serum TNF-α and IL-6. Immunohistochemistry confirmed fewer CD68+ and CD11b+ macrophages in CKD muscle. In conclusion, skeletal muscle collagen content is increased in humans with CKD and is associated with functional parameters. Muscle fibrosis correlated with increased FAP abundance, which may be due to insufficient macrophage-mediated TNF-α secretion. These data provide a foundation for future research elucidating the mechanisms responsible for this newly identified human muscle pathology.
肌肉功能障碍是慢性肾脏病(CKD)患者发病率的一个重要原因。虽然 CKD 啮齿动物模型中存在肌肉纤维化,但它在人类中的存在及其对身体功能的影响目前尚不清楚。我们检测了 CKD 患者(n=10)和健康、久坐不动的对照组(n=10)的等长腿伸肌力量以及骨骼肌纤维化和炎症的测量值。组织化学和免疫组织化学用于评估肌肉胶原和巨噬细胞和纤维/脂肪生成祖细胞(FAP)细胞群,实时定量 PCR 用于评估肌肉特异性炎症标志物的表达。与对照组相比,CKD 患者的肌肉胶原含量显著增加(18.8±2.1%与 11.7±0.7%胶原面积,P=0.008),I 型胶原、前胶原 I 和一种与重塑胶原结合的新型胶原杂交肽的染色也显著增加。CKD 患者的肌肉胶原与腿伸肌力量呈负相关(r=-0.74,P=0.01)。FAP 丰度在 CKD 中增加,与肌肉胶原高度相关(r=0.84,P<0.001),与 TNF-α 表达呈负相关(r=-0.65,P=0.003)。尽管 CKD 患者的血清 TNF-α和 IL-6 水平较高,但 CKD 患者的 TNF-α、CD68、CCL2 和 CCL5 mRNA 明显低于对照组。免疫组织化学证实 CKD 患者的肌肉中 CD68+和 CD11b+巨噬细胞较少。总之,CKD 患者的骨骼肌胶原含量增加,与功能参数相关。肌肉纤维化与 FAP 丰度增加相关,这可能是由于巨噬细胞介导的 TNF-α分泌不足所致。这些数据为阐明这种新发现的人类肌肉病理学的机制提供了基础。