Bhaisora Kamlesh Singh, Das Kuntal Kanti, Jamdar Janmejay, Behari Sanjay, Mehrotra Anant, Sardhara Jayesh, Srivastava Arun Kumar, Jaiswal Awadhesh Kumar, Sahu Rabi Narayan
Department of Neurosurgery, SGPGIMS, Lucknow, Uttar Pradesh, India.
Asian J Neurosurg. 2018 Jul-Sep;13(3):782-785. doi: 10.4103/1793-5482.238003.
Trans -sellar trans-sphenoidal encephalocele is an extremely rare entity. We present the case of an 18-month old boy who presented with a trans-sellar, trans-sphenoidal encephalocele associated with cleft lip, cleft palate and microphthalmia. This patient was treated successfully by a trans-cranial extra-dural route. In this paper, we discuss the clinico-radiological findings as well as various surgical options in managing these rare lesions and briefly review the literature.
经蝶鞍经蝶骨脑膨出是一种极为罕见的病症。我们报告一例18个月大的男孩,其患有经蝶鞍、经蝶骨脑膨出,并伴有唇裂、腭裂和小眼症。该患者通过经颅硬膜外途径成功治愈。在本文中,我们讨论了这些罕见病变的临床放射学表现以及各种手术治疗方案,并简要回顾了相关文献。