乳腺隆突性皮肤纤维肉瘤——一种罕见的疾病。
Dermatofibrosarcoma Protuberans of the Breast-a Rare Entity.
作者信息
Maji Suvendu, Paul M J, Sen Supriya
机构信息
1DNB Surgical Oncology, Chittaranjan National Cancer Institute, 37 SP Mukherjee Road, Kolkata, West Bengal 700026 India.
2Christian Medical College Vellore, Tamil Nadu, 632004 India.
出版信息
Indian J Surg Oncol. 2018 Sep;9(3):351-354. doi: 10.1007/s13193-017-0684-8. Epub 2017 Aug 10.
Dermatofibrosarcoma protuberans (DFSP) represents about 1% of soft-tissue sarcomas with an estimated incidence of 0.8 to 5.0 cases per million per year. This lesion may occur anywhere in the body but more than 50% occur on the trunk, 20% on the head and neck and 30% on the extremities. DFSP of the breast is an extremely uncommon site of presentation. Data regarding DFSP of the breast is limited and mostly in the form of case reports. Clinical presentation is not uniform and may mimic benign skin lesions [1]. However, it typically presents as a nodular cutaneous mass in early or mid-adult life. We herein report a case of DFSP of the breast in a 33-year-old lady who was managed successfully in our institute and review the literature associated with it.
隆突性皮肤纤维肉瘤（DFSP）约占软组织肉瘤的1%，估计发病率为每年每百万人口0.8至5.0例。该病变可发生于身体的任何部位，但超过50%发生于躯干，20%发生于头颈部，30%发生于四肢。乳腺DFSP是一种极其罕见的发病部位。关于乳腺DFSP的数据有限，且大多为病例报告形式。临床表现并不一致，可能类似良性皮肤病变[1]。然而，它通常在成年早期或中期表现为结节状皮肤肿物。我们在此报告一例33岁女性乳腺DFSP病例，该患者在我们研究所成功接受治疗，并对相关文献进行综述。
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