Al-Farsi Abeer, Al-Brashdi Aza, Al-Salhi Samyia, Al-Rahbi Nasser, Al-Rahbi Salim, Al-Masqari Mohammed, Al-Manji Zainab, Al-Umairi Rashid S
Department of Radiology, Oman Medical Specialty Board, Muscat, Oman.
Department of Radiology, the Royal Hospital, Muscat, Oman.
Sultan Qaboos Univ Med J. 2020 Aug;20(3):e368-e371. doi: 10.18295/squmj.2020.20.03.019. Epub 2020 Oct 5.
Dermatofibrosarcoma protuberans (DFSP) is a rare, slow-growing mesenchymal neoplasm of the dermis and subcutaneous tissues that has a low-to intermediate-grade malignancy. DFSP commonly involves the trunk and extremities, and very rarely the breast skin, mimicking a primary breast neoplasm with few reported cases in the literature. We report a 35-year old female patient who was referred to the Royal Hospital, Muscat, Oman in 2017, with a two-year history of a slow growing left breast lump. Assessment of the breasts with mammography revealed a lobulated lesion in the left-upper-inner quadrant with neither microcalcification nor architectural distortion, mimicking a benign lesion. However, on ultrasound, the lesion had suspicious features with increased vascularity and hence, it was categorised as breast imaging reporting and data system (BIRAD) IV. The patient underwent left breast wide local excision and the histopathological diagnosis was dermatofibrosarcoma protuberans.
隆突性皮肤纤维肉瘤（DFSP）是一种罕见的、生长缓慢的真皮和皮下组织间叶性肿瘤，恶性程度为低至中度。DFSP通常累及躯干和四肢，极少累及乳腺皮肤，易误诊为原发性乳腺肿瘤，文献报道的病例较少。我们报告一例35岁女性患者，2017年转诊至阿曼马斯喀特皇家医院，有左侧乳腺肿块缓慢生长两年的病史。乳房钼靶检查显示左乳内上象限有一个分叶状病变，无微钙化及结构扭曲，类似良性病变。然而，超声检查显示该病变具有可疑特征，血管增多，因此被分类为乳腺影像报告和数据系统（BIRAD）IV级。患者接受了左乳广泛局部切除，组织病理学诊断为隆突性皮肤纤维肉瘤。
