Gétaz E P, Staples W G, Lurie A
S Afr Med J. 1977 Oct 1;52(15):595-601.
The clinical and haematological features of haemophilia are reviewed and the historical aspects, pathogenesis and genetics are discussed. The problems associated with management, such as factor replacement, home therapy, physiotherapy, surgical intervention and the presence of inhibitors, are fully described. Finally, mention is made of the psychological problems of haemophiliacs and of the help given by the South African Haemophilia Foundation.
本文回顾了血友病的临床和血液学特征,并讨论了其历史背景、发病机制和遗传学。文中全面描述了与治疗相关的问题,如因子替代治疗、家庭治疗、物理治疗、手术干预以及抑制剂的存在。最后,提及了血友病患者的心理问题以及南非血友病基金会提供的帮助。