Department of Cardiovascular Surgery, Osaka Women's and Children's Hospital, Osaka, Japan.
Department of Cardiovascular Surgery, Osaka Women's and Children's Hospital, Osaka, Japan.
Ann Thorac Surg. 2019 May;107(5):e317-e319. doi: 10.1016/j.athoracsur.2018.08.079. Epub 2018 Oct 22.
We present a case of critical Ebstein's anomaly with circular shunting, diagnosed in utero. The fetal cardiothoracic area ratio was elevated; tricuspid regurgitation and pulmonary regurgitation worsened with fetal hydrops. At 35 weeks 6 days of gestation, elective caesarean section delivery was performed. Planned bilateral pulmonary artery banding and pulmonary trunk ligation were performed as a palliative operation 4 hours after birth, with the infant in a stable condition. At age 5 days, we performed the Starnes operation. The postoperative course was uneventful and a bidirectional Glenn operation was performed at age 4 months.
我们报告了一例先天性心脏病Ebstein 畸形(三尖瓣下移畸形)伴环形分流,于宫内诊断。胎儿心胸面积比升高,三尖瓣反流和肺动脉瓣反流随胎儿水肿加重。妊娠 35 周 6 天后行择期剖宫产术。出生后 4 小时,患儿生命体征平稳,行双侧肺动脉环缩术和肺动脉干结扎术姑息治疗。5 天时行 Starnes 手术。术后恢复顺利,4 月龄时行双向 Glenn 手术。