肝上皮样血管内皮瘤：一种极易误诊的疾病。
Hepatic epithelioid hemangioendothelioma: A great mimicker.
作者信息
Llueca Antoni, Piquer Dolors, Maazouzi Yasmine, Medina Carmen, Delgado Katty, Serra Anna, Escrig Javier
机构信息
Multidisciplinary Unit for Abdominal Pelvic Oncology Surgery (MUAPOS), University General Hospital of Castellon, Spain; Dept. of Medicine, University Jaume I (UJI), Castellon de la Plana, Spain.
Multidisciplinary Unit for Abdominal Pelvic Oncology Surgery (MUAPOS), University General Hospital of Castellon, Spain.
出版信息
Int J Surg Case Rep. 2018;53:25-28. doi: 10.1016/j.ijscr.2018.10.013. Epub 2018 Oct 12.
INTRODUCTION
Epithelioid hemangioendothelioma is a malignant mesenchymal tumor of unknown etiology. They tend to be asymptomatic or with non-specific symptoms. The lesion is usually multiple and variable size.
PRESENTATION OF CASE
We describe a clinical case of a 23-years-old patient diagnosed with a pelvic mass, a possible uterine fibroid or adnexal mass, and multiple liver lesions that seemed an advanced ovarian cancer presentation and after liver biopsy turned out to be a hepatic epithelioid hemangioendothelioma.
DISCUSSION
It may be confused with a metastatic process in diagnostic imaging. There have been described some possible risk factors but the etiology remains unknown. The prognosis is usually lethal in 50% of cases. The surgical removal of the lesion and liver transplant appear to be the only hope for these patients.
CONCLUSION
Epithelioid hemangioendothelioma must be part of our differential diagnosis when we find a liver tumour, especially in young women. Treatment is excision of the tumour in limited disease. In the case of unresectable disease are candidates for liver transplantation.
引言
上皮样血管内皮瘤是一种病因不明的恶性间叶性肿瘤。它们往往无症状或伴有非特异性症状。病变通常为多发且大小不一。
病例介绍
我们描述了一例23岁患者的临床病例，该患者被诊断为盆腔肿块，可能是子宫肌瘤或附件肿块，以及多个肝脏病变，看似晚期卵巢癌表现，经肝脏活检后发现是肝上皮样血管内皮瘤。
讨论
在诊断成像中它可能与转移过程相混淆。已经描述了一些可能的危险因素，但病因仍然不明。50%的病例预后通常是致命的。手术切除病变和肝移植似乎是这些患者唯一的希望。
结论
当我们发现肝脏肿瘤时，尤其是在年轻女性中，上皮样血管内皮瘤必须纳入我们的鉴别诊断。对于局限性疾病，治疗方法是切除肿瘤。对于不可切除的疾病，患者可考虑肝移植。
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