Aypak Cenk, Yıkılkan Hülya, Uysal Zekai, Görpelioğlu Süleyman
Department of Family Medicine, Dışkapı Yıldırım Beyazıt Teaching and Research Hospital, 06030 Ankara, Turkey.
Case Rep Med. 2012;2012:942074. doi: 10.1155/2012/942074. Epub 2012 May 27.
Unilateral absence of the pulmonary artery (UAPA) or pulmonary artery agenesis is a rare congenital disorder presenting with a wide spectrum of symptoms. UAPA is usually associated with cardiac anomalies and surgically treated in childhood. We report a rare case of a 50-year-old woman who was diagnosed with left pulmonary artery agenesis without any other cardiac anomalies. Clinicians should be aware of the possibility of undiagnosed cases of UAPA in patients through a chest radiograph that suggests the diagnosis. Confirmation of the diagnosis and anatomic details can be discerned by CT scanning.
单侧肺动脉缺如（UAPA）或肺动脉发育不全是一种罕见的先天性疾病，症状表现多样。UAPA通常与心脏异常有关，在儿童期接受手术治疗。我们报告一例罕见病例，一名50岁女性被诊断为左肺动脉发育不全，无任何其他心脏异常。临床医生应通过胸部X线片提示诊断，意识到患者中存在未确诊的UAPA病例的可能性。通过CT扫描可明确诊断及解剖细节。
