Santos Flávia da Silva Domingos, Grupioni Priscila Vinhal, Towersey Loan, Bernardes Filho Fred
Department of Internal Medicine, São Francisco Hospital, Ribeirão Preto, SP, Brasil.
Department of Oncology, São Francisco Hospital, Ribeirão Preto, SP, Brasil.
Rev Assoc Med Bras (1992). 2018 Dec;64(12):1073-1074. doi: 10.1590/1806-9282.64.12.1073.
Granulocytic sarcoma also called myeloid sarcoma is an extramedullary tumour of immature granulocytic cells. It is a rare entity, and mostly accompanied by acute myeloid leukaemia. It is observed during the course of myeloproliferative disorders especially in chronic myeloid leukaemia and myelodysplastic syndromes.
Here, we report a case of a 60-year-old male with past history of myelofibrosis admitted to the emergency room due ulceronecrotic lesions, fever and dysphagia. We emphasize the importance of recognizing this entity and its severity.
粒细胞肉瘤又称髓细胞肉瘤,是未成熟粒细胞的髓外肿瘤。它是一种罕见的疾病,大多伴有急性髓系白血病。在骨髓增殖性疾病过程中可见,尤其是在慢性髓系白血病和骨髓增生异常综合征中。
在此,我们报告一例60岁男性,既往有骨髓纤维化病史,因溃疡坏死性病变、发热和吞咽困难入住急诊室。我们强调认识这一疾病及其严重性的重要性。