Department of Cell and Developmental Biology, University of Colorado School of Medicine, Aurora, Colorado.
Glia. 2019 Apr;67(4):650-667. doi: 10.1002/glia.23559. Epub 2019 Jan 9.
Demyelination occurs following many neurological insults, most notably in multiple sclerosis (MS). Therapeutics that promote remyelination could slow the neurological decline associated with chronic demyelination; however, in vivo testing of candidate small molecule drugs and signaling cascades known to impact myelination is expensive and labor intensive. Here, we describe the development of a novel zebrafish line which uses the putative promoter of Myelin Protein Zero (mpz), a major structural protein in myelin, to drive expression of Enhanced Green Fluorescent Protein (mEGFP) specifically in the processes and nascent internodes of myelinating glia. We observe that changes in fluorescence intensity in Tg(mpz:mEGFP) larvae are a reliable surrogate for changes in myelin membrane production per se in live larvae following bath application of drugs. These changes in fluorescence are strongly predictive of changes in myelin-specific mRNAs [mpz, 36K and myelin basic protein (mbp)] and protein production (Mbp). Finally, we observe that certain drugs alter nascent internode number and length, impacting the overall amount of myelin membrane synthesized and a number of axons myelinated without significantly changing the number of myelinating oligodendrocytes. These studies demonstrate that the Tg(mpz:mEGFP) reporter line responds effectively to positive and negative small molecule regulators of myelination, and could be useful for identifying candidate drugs that specifically target myelin membrane production in vivo. Combined with high throughput cell-based screening of large chemical libraries and automated imaging systems, this transgenic line is useful for rapid large scale whole animal screening to identify novel myelinating small molecule compounds in vivo.
髓鞘脱失发生在许多神经损伤后,尤其是多发性硬化症(MS)。促进髓鞘再生的治疗方法可以减缓与慢性脱髓鞘相关的神经衰退;然而,体内测试已知可影响髓鞘形成的候选小分子药物和信号级联反应既昂贵又费力。在这里,我们描述了一种新型斑马鱼系的开发,该系使用髓鞘蛋白零(mpz)的假定启动子,髓鞘中的主要结构蛋白,特异性地在髓鞘形成的神经胶质的过程和新生节段中驱动增强型绿色荧光蛋白(mEGFP)的表达。我们观察到,在药物浴处理后,Tg(mpz:mEGFP)幼虫中荧光强度的变化本身就是髓鞘膜产生变化的可靠替代物。这些荧光变化强烈预示着髓鞘特异性 mRNAs [mpz、36K 和髓鞘碱性蛋白 (mbp)]和蛋白质产生(Mbp)的变化。最后,我们观察到某些药物改变新生节段的数量和长度,影响合成的髓鞘膜总量和许多被髓鞘化的轴突数量,而不显著改变髓鞘化少突胶质细胞的数量。这些研究表明,Tg(mpz:mEGFP)报告系对髓鞘形成的正、负小分子调节剂有效反应,并可用于鉴定特异性靶向体内髓鞘膜产生的候选药物。与高通量基于细胞的大型化学文库筛选和自动化成像系统相结合,这种转基因系可用于快速大规模全动物筛选,以鉴定体内新型髓鞘形成小分子化合物。