Doroudinia Abtin, Ahmadi Sara, Mehrian Payam, Pourabdollah Mihan
PET/CT, Chronic Respiratory Diseases Research Center, National Research Institute of Tuberculosis and Lung Diseases (NRITLD), Shahid Beheshti University of Medical Sciences, Tehran, The Islamic Republic of Iran.
Radiology, Telemedicine Research Center (TRC), National Research Institute of Tuberculosis and Lung Diseases (NRITLD), Shahid Beheshti University of Medical Sciences, Tehran, The Islamic Republic of Iran.
BMJ Case Rep. 2019 Jan 28;12(1):bcr-2018-227198. doi: 10.1136/bcr-2018-227198.
Primary Ewing sarcoma (ES) or primitive neuroectodermal tumour (PNET) is a rare tumour in adults and primary renal involvement is extremely rare. Patients with renal ES or PNET respond to and would benefit from conventional ES treatment according to ES study protocols. Here, we report a case of a young woman, presenting with right flank pain and haematuria. After ultrasound and CT evaluation, a right middle pole renal mass was detected. The patient underwent radical right nephrectomy, and a grade 4 ES with peritoneal involvement was documented. Subsequently, the patient underwent adjuvant chemotherapy for 5 months. Follow-up 18F-fluorodeoxyglucose (FDG) positron emission tomography (PET)/CT scan demonstrated bilateral cervical, hilar, mediastinal and retroperitoneal FDG-avid adenopathies associated with mild right-sided pleural effusion with no metabolic activity, signifying the role of PET/CT scan in tumour restaging.
原发性尤因肉瘤（ES）或原始神经外胚层肿瘤（PNET）在成人中是一种罕见肿瘤，而原发性肾脏受累极为罕见。根据ES研究方案，患有肾脏ES或PNET的患者对传统ES治疗有反应且会从中受益。在此，我们报告一例年轻女性病例，该患者表现为右侧胁腹疼痛和血尿。经超声和CT评估后，检测到右肾中极有一肿块。患者接受了根治性右肾切除术，术后病理记录为4级ES伴腹膜受累。随后，患者接受了5个月的辅助化疗。随访的18F-氟脱氧葡萄糖（FDG）正电子发射断层扫描（PET）/CT显示双侧颈部、肺门、纵隔和腹膜后有FDG摄取阳性的淋巴结肿大，伴有右侧轻度胸腔积液且无代谢活性，这表明PET/CT扫描在肿瘤再分期中的作用。
