Ozturk Hakan
Department of Urology, School of Medicine, Sifa University, Izmir-Turkey.
Can Urol Assoc J. 2015 Jan-Feb;9(1-2):E39-44. doi: 10.5489/cuaj.2286.
Primitive peripheral neuroectodermal tumour and Ewing's sarcoma (PNET/EWS) were originally described as two distinct pathologic entities, although both share common stem-cell precursor and unique chromosomal abnormality. Although its incidence has increased recently, its share in all sarcomas is 1%. It is usually seen in men and women in their twenties. We present a case of a 38-year-old woman with a left renal mass detected incidentally. Magnetic resonance imaging revealed a centrally located hypervascular renal mass with diameter of 6 cm with non-homogenous contrast enhancement containing necrotic and calcific areas. The patient was diagnosed as having PNET/EWS by histopathological examination following radical nephrectomy. Para-aortic lymph node metastasis was found on imaging by (18)F-fluorodeoxyglucose (FDG)-positron-emission tomography/computed tomography (PET/CT).
原始外周神经外胚层肿瘤和尤因肉瘤（PNET/EWS）最初被描述为两种不同的病理实体，尽管它们具有共同的干细胞前体和独特的染色体异常。虽然其发病率最近有所上升，但其在所有肉瘤中的占比为1%。它通常见于二十多岁的男性和女性。我们报告一例38岁女性，偶然发现左肾肿块。磁共振成像显示一个位于中央的高血管性肾肿块，直径6厘米，增强扫描不均匀，包含坏死和钙化区域。患者在根治性肾切除术后经组织病理学检查诊断为PNET/EWS。通过（18）F-氟脱氧葡萄糖（FDG）-正电子发射断层扫描/计算机断层扫描（PET/CT）成像发现腹主动脉旁淋巴结转移。
