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视网膜中央静脉阻塞揭示腹腔疾病

Central Retinal Vein Occlusion Revealing Coeliac Disease.

作者信息

Zoubeidi Hana, Ben Salem Thouraya, Ben Ghorbel Imed, Houman Mohamed Habib

机构信息

Department of Internal Medicine, Rabta Hospital, Tunis, Tunisia.

出版信息

Eur J Case Rep Intern Med. 2016 Sep 20;3(7):000492. doi: 10.12890/2016_000492. eCollection 2016.

Abstract

INTRODUCTION

Thrombosis has been widely reported in coeliac disease (CD) but central retinal vein occlusion (CRVO) is rarely described.

CASE PRESENTATION

A 27-year-old woman presented with acute visual loss and was diagnosed with CRVO. Her protein S and protein C levels were low and CD was diagnosed on the basis of endoscopic, immunological and histological results. A gluten-free diet resulted in favourable evolution.

CONCLUSION

CD should be considered in young patients with thrombosis, especially if in an unusual location. Treatment is based on a gluten-free diet.

LEARNING POINTS

Coeliac disease (CD) should be considered in young patients with central retinal vein occlusion (CRVO).Several mechanisms can cause thrombosis in CD.CRVO in CD is often reversible with a gluten-free diet.

摘要

引言

血栓形成在乳糜泻(CD)中已有广泛报道,但中央视网膜静脉阻塞(CRVO)鲜有描述。

病例报告

一名27岁女性因急性视力丧失就诊,被诊断为CRVO。她的蛋白S和蛋白C水平较低,根据内镜、免疫学和组织学结果诊断为CD。无麸质饮食使病情向好发展。

结论

对于患有血栓形成的年轻患者,尤其是血栓形成部位不寻常时,应考虑CD。治疗以无麸质饮食为基础。

经验教训

年轻的中央视网膜静脉阻塞(CRVO)患者应考虑乳糜泻(CD)。CD中有几种机制可导致血栓形成。CD中的CRVO通常通过无麸质饮食可逆转。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ff89/6346767/e0175c117fb9/492_Fig1.jpg

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