一种易导致反复肺炎的弯刀综合征异常变体。

An unusual variant of scimitar syndrome predisposing to recurrent pneumonia.

作者信息

Jackson Niki, Nokes Brandon T, Sakata Kenneth, Cummings Kristopher, Vaszar Laszlo

机构信息

The Department of Internal Medicine, Mayo Clinic, Phoenix, AZ, USA.

Division of Pulmonary, Critical Care, and Sleep Medicine, University of California, San Diego, USA.

出版信息

Respir Med Case Rep. 2019 Jan 23;26:240-243. doi: 10.1016/j.rmcr.2019.01.010. eCollection 2019.

DOI:10.1016/j.rmcr.2019.01.010

PMID:30775240

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC6366150/

Abstract

Scimitar syndrome is a rare constellation of congenital conditions pertaining to partial anomalous pulmonary venous return. Radiographically, these anomalous pulmonary veins can resemble a scimitar, and have heterogeneous clinical presentations. We present an unusual case of scimitar syndrome with associated recurrent pneumonia. We will briefly review the literature on scimitar syndrome as well as discuss how a predisposition to recurrent pneumonia may develop in this unusual variant of a rare clinical entity.

摘要

弯刀综合征是一种罕见的先天性疾病组合，与部分肺静脉异常回流有关。在影像学上，这些异常肺静脉可类似弯刀，且临床表现具有异质性。我们报告一例伴有复发性肺炎的罕见弯刀综合征病例。我们将简要回顾关于弯刀综合征的文献，并讨论在这种罕见临床实体的不寻常变体中复发性肺炎的易患因素是如何形成的。