Primary alveolar rhabdomyosarcoma of retrorectal-presacral space in an adult patient: A case report of an uncommon tumor with rare presentation.

RATIONALE

Rhabdomyosarcoma (RMS) has known as a highly malignant soft tissue sarcoma, representing 5% to 10% of all solid tumors in childhood. Alveolar rhabdomyosarcoma (ARMS) of the retrorectal-presacral space is an extremely rare lesion for adult, no study has been reported in the English literature.

PATIENT CONCERNS

A 51-year-old male presented with abdominal pain for 1 month, significantly worse when having a bowel movement.

DIAGNOSIS

Computed tomography (CT) and magnetic resonance imaging (MRI) of the pelvis showed a solid-cystic, enhancing lesion of dimension located in retrorectal-presacral space. The surgical specimen was reported as ARMS after pathological evaluation.

INTERVENTIONS

The tumor was complete surgical resection, and after surgery, the patient was treated with combination chemotherapy.

OUTCOMES

At 23 months follow up, the patient was asymptomatic with no evidence of metastases or local recurrence.

LESSONS

Improvements in imaging in addition to early surgical intervention and chemotherapy treatment are crucial to improve survival chances against RMS.