Gussago S, Spina P, Guerra A
Ospedale Regionale di Bellinzona e Valli, Surgery Department, Bellinzona, Switzerland.
Cantonal Institute of Pathology, Locarno, Switzerland.
J Surg Case Rep. 2019 Mar 13;2019(3):rjz057. doi: 10.1093/jscr/rjz057. eCollection 2019 Mar.
Benign Multicystic Peritoneal Mesothelioma (BMPM) is a rare benign cystic neoplasm that arise from the peritoneum, typically found in young females (83%), with a high incidence of local recurrence after resection (almost 50% of cases). Fewer than 200 cases have been reported worldwide in 2017. Due to its rarity and the lack of a classical clinical presentation, the diagnosis pre-operatively is challenging; moreover a great part of the literature is composed of case reports and small group studies. Nowadays, guidelines are still not available, and treatment is en bloc resection of the lesion. Some authors suggest the use of Hyperthermic Intraperitoneal Chemotherapy (HIPEC) associated with the surgical approach, even if comparative data on recurrence and complications are lacking. We report a case of BMPM diagnosed in a 40-year-old male who underwent an exploratory laparoscopy and complete excision of the neoformation. Pathology confirmed the presence of a BMPM.
良性多囊性腹膜间皮瘤(BMPM)是一种罕见的良性囊性肿瘤,起源于腹膜,多见于年轻女性(83%),切除术后局部复发率高(近50%的病例)。2017年全球报告的病例不足200例。由于其罕见性以及缺乏典型的临床表现,术前诊断具有挑战性;此外,大部分文献由病例报告和小样本研究组成。目前,仍没有相关指南,治疗方法是整块切除病灶。一些作者建议在手术治疗的同时联合使用腹腔内热灌注化疗(HIPEC),尽管缺乏关于复发和并发症的对比数据。我们报告一例40岁男性被诊断为BMPM的病例,该患者接受了探查性腹腔镜检查并完整切除了新生物。病理检查证实为BMPM。