Department of Ocular Oncology, Centre for Sight, Asoka Capitol Building, Road No 2, Banjara Hills, Hyderabad, Telangana, India.
Department of Ocular Pathology, Centre for Sight, Asoka Capitol Building, Road No 2, Banjara Hills, Hyderabad, Telangana, India.
Indian J Ophthalmol. 2019 Apr;67(4):568-570. doi: 10.4103/ijo.IJO_633_18.
An 18-year-old female presented with rapidly progressive proptosis of the left eye for one month and grade II relative afferent pupillary defect. Orbital imaging showed a well-defined homogenous extraconal mass in close relation to the lateral rectus muscle and extending up to the superior orbital fissure, associated with bony erosion. An incisional biopsy was performed, with the histopathology demonstrating stellate to spindle-shaped tumor cells (fibroblasts) embedded in a richly myxoid matrix. A diagnosis of low-grade fibromyxoid sarcoma (LGFS) was made. The patient was treated by stereotactic external beam radiotherapy. Here, we report a case of LGFS which, to the best of our knowledge, is the first at an orbital location.
一位 18 岁女性因左眼进行性眼球突出伴 II 级相对性传入性瞳孔障碍就诊，病程 1 个月。眼眶影像学检查显示，外侧直肌附近有一个边界清楚的均匀眶外肿块，延伸至眶上裂，伴有骨侵蚀。行切开活检，组织病理学显示星状至梭形肿瘤细胞（成纤维细胞）嵌入丰富的黏液样基质中。诊断为低度纤维黏液样肉瘤（LGFS）。患者接受立体定向外照射放疗。据我们所知，这是首例发生在眼眶部位的 LGFS 病例。
