New York Presbyterian Hospital-Weill Cornell Medical Center, New York, NY, USA.
New York Presbyterian Hospital-Weill Cornell Medical Center, New York, NY, USA.
Clin Imaging. 2019 Jul-Aug;56:77-80. doi: 10.1016/j.clinimag.2019.03.008. Epub 2019 Mar 13.
Juvenile granulosa cell tumor (JGCT) is an extremely rare ovarian tumor that has been associated with Maffucci syndrome. It both secretes hormone and has been postulated to grow in response to hormone. We present a case of a 33-year-old G1P0 asymptomatic woman with a history of Maffucci syndrome found to have a left adnexal mass on routine ultrasonography at 13 weeks gestation. This case demonstrates the sonographic and magnetic resonance imaging (MRI) features of JGCT, as well as the natural progression of the tumor during pregnancy. A follow-up ultrasound 3 weeks after initial diagnosis demonstrated marked growth in size and vascularity of the tumor, prompting unilateral salpingo-oophorectomy. Histopathological findings confirmed the diagnosis of JGCT.
幼年颗粒细胞瘤（JGCT）是一种极其罕见的卵巢肿瘤，与马富奇综合征有关。它既能分泌激素，又被认为是激素反应性生长的。我们报告了一例 33 岁 G1P0 无症状妇女，有马富奇综合征病史，在 13 周妊娠时常规超声检查发现左侧附件肿块。该病例显示了 JGCT 的超声和磁共振成像（MRI）特征，以及肿瘤在怀孕期间的自然进展。最初诊断后 3 周的超声随访显示肿瘤大小和血管明显增大，促使行单侧输卵管卵巢切除术。组织病理学检查结果证实了 JGCT 的诊断。
