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大动脉炎中的肾病范围蛋白尿和代谢性碱中毒

Nephrotic range proteinuria and metabolic alkalosis in Takayasu arteritis.

作者信息

Tsuchida Takahiro, Yano Hiroyuki, Raita Yoshihiko, Kinjo Mitsuyo

机构信息

Department of Internal Medicine, Okinawa Chubu Hospital, Uruma, Japan.

出版信息

BMJ Case Rep. 2019 Apr 15;12(4):e228637. doi: 10.1136/bcr-2018-228637.

Abstract

Nephrotic range proteinuria and metabolic alkalosis are unusual findings in large vessel vasculitis. In this case, renovascular hypertension with unilateral renal artery stenosis in Takayasu arteritis was complicated by nephrotic range proteinuria. Symptoms resolved after angioplasty, although non-nephrotic proteinuria persisted. The renal pathology of Takayasu arteritis included focal glomerulosclerosis.

摘要

肾病范围蛋白尿和代谢性碱中毒在大血管血管炎中是不常见的表现。在该病例中,高安动脉炎伴肾血管性高血压和单侧肾动脉狭窄并发了肾病范围蛋白尿。血管成形术后症状缓解,尽管非肾病范围蛋白尿持续存在。高安动脉炎的肾脏病理表现包括局灶性肾小球硬化。

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本文引用的文献

1
Kidney involvement in medium- and large-vessel vasculitis.中、大血管血管炎中的肾脏受累情况。
J Nephrol. 2016 Aug;29(4):495-505. doi: 10.1007/s40620-016-0303-8. Epub 2016 Apr 20.
3
Causes and pathogenesis of focal segmental glomerulosclerosis.局灶节段性肾小球硬化的病因及发病机制。
Nat Rev Nephrol. 2015 Feb;11(2):76-87. doi: 10.1038/nrneph.2014.216. Epub 2014 Dec 2.
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Glomerular disease associated with Takayasu arteritis: 6 cases analysis and review of the literature.
Chin Med Sci J. 2009 Jun;24(2):69-75. doi: 10.1016/s1001-9294(09)60063-8.
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Takayasu arteritis: association with focal segmental glomerulosclerosis.
Clin Rheumatol. 2007 Apr;26(4):609-11. doi: 10.1007/s10067-005-0190-1. Epub 2006 Feb 22.

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