Tsuchida Takahiro, Yano Hiroyuki, Raita Yoshihiko, Kinjo Mitsuyo
Department of Internal Medicine, Okinawa Chubu Hospital, Uruma, Japan.
BMJ Case Rep. 2019 Apr 15;12(4):e228637. doi: 10.1136/bcr-2018-228637.
Nephrotic range proteinuria and metabolic alkalosis are unusual findings in large vessel vasculitis. In this case, renovascular hypertension with unilateral renal artery stenosis in Takayasu arteritis was complicated by nephrotic range proteinuria. Symptoms resolved after angioplasty, although non-nephrotic proteinuria persisted. The renal pathology of Takayasu arteritis included focal glomerulosclerosis.
肾病范围蛋白尿和代谢性碱中毒在大血管血管炎中是不常见的表现。在该病例中,高安动脉炎伴肾血管性高血压和单侧肾动脉狭窄并发了肾病范围蛋白尿。血管成形术后症状缓解,尽管非肾病范围蛋白尿持续存在。高安动脉炎的肾脏病理表现包括局灶性肾小球硬化。