Singhal Roopesh
Department of Cardiology,U. N. Mehta Institute of Cardiology and Research Center,Civil Hospital Campus, Asarwa, Ahmedabad, Gujarat,India.
Cardiol Young. 2019 May;29(5):704-707. doi: 10.1017/S1047951119000271. Epub 2019 Apr 30.
Unilateral interruption of pulmonary artery is a rare congenital anomaly which is usually associated with other congenital heart disease. Even more rarely it may occur in isolation. Most of the cases are incidentally detected in adulthood. Some cases develop pulmonary hypertension for yet unknown reasons; such cases usually present in infancy with right heart failure. Surgical correction in such cases is associated with adverse outcomes. Heart lung transplantation should be considered in such patients. We report a 3-year-old boy with interruption of right pulmonary artery with severe pulmonary hypertension and right heart failure who was considered for heart lung transplantation.
单侧肺动脉中断是一种罕见的先天性异常，通常与其他先天性心脏病相关。甚至更罕见的是，它可能单独出现。大多数病例是在成年期偶然发现的。一些病例会出现原因不明的肺动脉高压；这类病例通常在婴儿期出现右心衰竭。此类病例的手术矫正会带来不良后果。对于这类患者应考虑进行心肺移植。我们报告了一名3岁男孩，患有右肺动脉中断并伴有严重肺动脉高压和右心衰竭，该患儿被考虑进行心肺移植。
