Herraiz Sarachaga I, Pérez González W, Vergara Rodríguez F, Alonso Lastra M J, Acerete Guillén F, Bermúdez-Cañete Fernández R, Díaz García P, Quero Jiménez M
Servicio de Cardiología Pediátrica, Hospital Ramón y Cajal, Madrid.
An Esp Pediatr. 1993 Feb;38(2):139-44.
We present our experience with four cases of unilateral pulmonary agenesis, 3 of the right artery and the other one of the left. Two of the patients had pulmonary hypertension and one of them died at two years of age. All cases were diagnosed by using pulmonary angiography. Aortography demonstrated the absence of circulatory supply to the lung and a contralateral aortic arch to the absent pulmonary artery. We have performed a review of the literature with an emphasis on the diagnostic aspects of this condition, and discuss the considerations for possible surgery in symptomatic patients.
我们介绍了4例单侧肺发育不全的病例经验，其中3例为右肺动脉发育不全，1例为左肺动脉发育不全。2例患者患有肺动脉高压，其中1例在2岁时死亡。所有病例均通过肺血管造影确诊。主动脉造影显示患侧肺无循环供血，且在缺如肺动脉的对侧有主动脉弓。我们对文献进行了综述，重点关注该疾病的诊断方面，并讨论了有症状患者可能的手术考量。
