前腹壁转移性恶性颗粒细胞瘤（阿布里科索夫瘤），生存期延长
Metastasizing Malignant Granular Cell Tumor (Abrikossoff Tumor) of the Anterior Abdominal Wall, with Prolonged Survival.
作者信息
Alnashwan Yara A, Ali Khaled A H, Amr Samir S
机构信息
Department of Pathology, Faculty of Medicine, Imam Abdulrahman Bin Faisal University, Dammam, Saudi Arabia.
Department of Pathology, Almana General Hospital, Dammam, Saudi Arabia.
出版信息
Case Rep Pathol. 2019 Apr 7;2019:9576487. doi: 10.1155/2019/9576487. eCollection 2019.
Malignant granular cell tumor (MGCT) is a rare high-grade mesenchymal tumor of Schwann cell origin. MGCTs commonly affect thigh, extremity, and trunk; however, involvement of the abdominal wall is quite rare. It has poor prognosis with 39% mortality rate in 3-year interval. We report a 50-year-old female who had MGCT arising in the anterior abdominal wall and developed massive metastatic deposits in both lungs and in the right inguinal lymph nodes, with prolonged survival for 11 years. A brief review of the literature is presented.
恶性颗粒细胞瘤（MGCT）是一种罕见的起源于施万细胞的高级别间充质肿瘤。MGCT通常累及大腿、四肢和躯干；然而，累及腹壁的情况相当罕见。其预后较差，3年间隔期死亡率为39%。我们报告一名50岁女性，其腹壁前部发生MGCT，并在双肺和右侧腹股沟淋巴结出现大量转移灶，生存期延长至11年。本文对相关文献进行简要综述。
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