Ahlgren L S
J Pediatr Surg. 1987 May;22(5):451-3. doi: 10.1016/s0022-3468(87)80268-3.
Apple peel deformity of the small bowel is a variant of jejunal atresia with a high mortality. Forty five percent of these patients can be expected to die, most from anastomotic leaks with sepsis, or anastomotic failure with prolonged ileus and malnutrition. This report documents survival of three consecutive patients treated by an adaptation of the Santulli "chimney" anastomosis. This method accomplishes the goals of relief of intestinal obstruction, minimal resection, and preservation of tenuous intestinal blood vessels. All three patients had a benign postoperative course and made an uneventful recovery. Intestinal function is normal in each patient at 1 1/2 years. Based on this experience, it appears that a Santulli jejunojejunostomy combined with total parenteral nutrition offers the most promising operative strategy in the treatment of patients with apple peel bowel.
小肠苹果皮样畸形是空肠闭锁的一种变体,死亡率很高。预计这些患者中有45%会死亡,大多数死于吻合口漏伴败血症,或吻合口失败伴长期肠梗阻和营养不良。本报告记录了连续3例采用改良桑图利“烟囱”吻合术治疗患者的存活情况。该方法实现了缓解肠梗阻、最小限度切除以及保留脆弱肠血管的目标。所有3例患者术后病程均平稳,恢复顺利。每位患者在1.5岁时肠道功能均正常。基于这一经验,桑图利空肠空肠吻合术联合全肠外营养似乎是治疗苹果皮样小肠患者最有前景的手术策略。