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四叶式主动脉瓣:两例报告及简要综述

Quadricuspid Aortic Valve: Report of Two Cases and Brief Review.

作者信息

Oladiran Oreoluwa, Nwosu Ifeanyi, Dhital Rashmi, Ezioma Gbujie

机构信息

Reading Hospital, Tower Health System, West Reading, Pennsylvania, USA.

Leighton Hospital NHS Trust, Crewe, Cheshire, UK.

出版信息

Case Rep Cardiol. 2019 Apr 9;2019:7835287. doi: 10.1155/2019/7835287. eCollection 2019.

DOI:10.1155/2019/7835287
PMID:31093380
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC6481097/
Abstract

Quadricuspid aortic valve (QAV) is a rare congenital cardiac defect characterized by the presence of four aortic valve leaflets of equal or varying sizes. Even rarer is its clinical presentation with aortic stenosis. Diagnosis of QAV could be challenging but is of great importance as patients often present with progressive aortic regurgitation. We present 2 cases of QAV presenting differently: one with aortic stenosis requiring valve replacement and the other with aortic regurgitation requiring close monitoring.

摘要

四叶式主动脉瓣(QAV)是一种罕见的先天性心脏缺陷,其特征是存在四个大小相等或不等的主动脉瓣叶。更为罕见的是其伴有主动脉狭窄的临床表现。QAV的诊断可能具有挑战性,但非常重要,因为患者常表现为进行性主动脉瓣反流。我们报告2例表现不同的QAV病例:1例患有主动脉狭窄需要进行瓣膜置换,另1例患有主动脉瓣反流需要密切监测。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/166d/6481097/69478d106308/CRIC2019-7835287.003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/166d/6481097/4004dcb2ef7b/CRIC2019-7835287.001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/166d/6481097/2db2329ade7e/CRIC2019-7835287.002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/166d/6481097/69478d106308/CRIC2019-7835287.003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/166d/6481097/4004dcb2ef7b/CRIC2019-7835287.001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/166d/6481097/2db2329ade7e/CRIC2019-7835287.002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/166d/6481097/69478d106308/CRIC2019-7835287.003.jpg

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Cardiol Res. 2017 Aug;8(4):169-171. doi: 10.14740/cr567w. Epub 2017 Aug 23.
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Quadricuspid Aortic Valve: A Case Report and Review of the Literature.四叶式主动脉瓣:一例病例报告及文献综述
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Quadricuspid Aortic Valve: A Comprehensive Review.四叶式主动脉瓣:全面综述
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Quadricuspid aortic valve and anomalous origin of the left circumflex coronary artery in a young man with Down syndrome.一名患有唐氏综合征的年轻男性的四叶式主动脉瓣和左旋支冠状动脉异常起源。
Clin Case Rep. 2015 Apr;3(4):271-3. doi: 10.1002/ccr3.126. Epub 2015 Feb 13.
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