Oladiran Oreoluwa, Nwosu Ifeanyi, Dhital Rashmi, Ezioma Gbujie
Reading Hospital, Tower Health System, West Reading, Pennsylvania, USA.
Leighton Hospital NHS Trust, Crewe, Cheshire, UK.
Case Rep Cardiol. 2019 Apr 9;2019:7835287. doi: 10.1155/2019/7835287. eCollection 2019.
Quadricuspid aortic valve (QAV) is a rare congenital cardiac defect characterized by the presence of four aortic valve leaflets of equal or varying sizes. Even rarer is its clinical presentation with aortic stenosis. Diagnosis of QAV could be challenging but is of great importance as patients often present with progressive aortic regurgitation. We present 2 cases of QAV presenting differently: one with aortic stenosis requiring valve replacement and the other with aortic regurgitation requiring close monitoring.
四叶式主动脉瓣(QAV)是一种罕见的先天性心脏缺陷,其特征是存在四个大小相等或不等的主动脉瓣叶。更为罕见的是其伴有主动脉狭窄的临床表现。QAV的诊断可能具有挑战性,但非常重要,因为患者常表现为进行性主动脉瓣反流。我们报告2例表现不同的QAV病例:1例患有主动脉狭窄需要进行瓣膜置换,另1例患有主动脉瓣反流需要密切监测。