Bennett W G, Watson R A, Heard J K, Vesely D L
Department of Internal Medicine, University of Arkansas for Medical Sciences, Little Rock.
Am J Gastroenterol. 1987 Oct;82(10):1091-5.
Common variable hypogammaglobulinemia (immunodeficiency), a disorder characterized by late-onset immunoglobulin deficiency and lack of humoral immunity, has a variable association with bronchiectasis, cholelithiasis, nodular lymphoid hyperplasia, gastrointestinal neoplasia, megaloblastic anemia, and malabsorption. The patient described in this report had all of the above except neoplasia. In addition, he had calcium oxalate renal stones probably secondary to his malabsorption. The first case demonstrating the beneficial effect of home hyperalimentation in patients with severe malabsorption refractory to other treatments is described. Home hyperalimentation overnight allows the patient freedom for daily activities while also being more cost-effective than in-hospital parenteral nutrition.
普通可变型低丙种球蛋白血症（免疫缺陷）是一种以迟发性免疫球蛋白缺乏和体液免疫缺乏为特征的疾病，与支气管扩张、胆结石、结节性淋巴组织增生、胃肠道肿瘤、巨幼细胞贫血和吸收不良有不同程度的关联。本报告中描述的患者除肿瘤外具备上述所有情况。此外，他患有草酸钙肾结石，可能继发于吸收不良。本文描述了首例证明家庭胃肠外营养对其他治疗无效的严重吸收不良患者有益的病例。夜间家庭胃肠外营养使患者在白天可自由进行日常活动，同时也比住院肠外营养更具成本效益。
