Neromyliotis Eleftherios, Sapountzi Marilia, Nikas Ioannis, Karydakis Ploutarchos, Mitsios Andreas, Sfakianos George, Themistocleous Marios S
Department of Neurosurgery, Children's Hospital 'Agia Sofia', Athens, Greece.
ENT Department, Children's Hospital 'Agia Sofia', Athens, Greece.
Oxf Med Case Reports. 2019 May 31;2019(5):omz039. doi: 10.1093/omcr/omz039. eCollection 2019 May.
Fibrous dysplasia is a rare non-malignant condition where fibrous tissue replaces the normal bone architecture. Involvement of temporal and occipital bones is exceptionally rare and is associated with unique complications. A 10-year-old boy presented with right retroauricular enlargement and pain. Imaging studies and biopsy revealed fibrous dysplasia of the temporal and occipital bones. There was no hearing loss or sequelae arising from posterior fossa compression. The patient was discharged with follow-up instructions. Only 10 cases of occipital bone fibrous dysplasia have been reported in the medical literature. Occipital bone fibrous dysplasia can be complicated with Chiari malformation and syringomyelia while temporal bone involvement is associated with hearing loss. These potential developments require close follow-up that includes detailed neurologic examination, imaging and audiology.
骨纤维异常增殖症是一种罕见的非恶性疾病，其中纤维组织取代了正常的骨骼结构。颞骨和枕骨受累极为罕见，且伴有独特的并发症。一名10岁男孩出现右耳后肿大和疼痛。影像学检查和活检显示颞骨和枕骨骨纤维异常增殖症。没有因后颅窝受压导致的听力丧失或后遗症。患者出院时带有随访指示。医学文献中仅报道了10例枕骨骨纤维异常增殖症病例。枕骨骨纤维异常增殖症可并发Chiari畸形和脊髓空洞症，而颞骨受累与听力丧失有关。这些潜在的病情发展需要密切随访，包括详细的神经系统检查、影像学检查和听力检查。
