Moussa Achraf, Adraoui Amine, Haouane Mohamed Amine, Ounjar Adil, Akhaddar Ali, Belfquih Hatim
Department of Neurosurgery, Avicenne Military Hospital, Cadi Ayyad University, Marrakech, MAR.
Department of Pathology, Avicenne Military Hospital, Cadi Ayyad University, Marrakech, MAR.
Cureus. 2025 Jul 18;17(7):e88246. doi: 10.7759/cureus.88246. eCollection 2025 Jul.
Fibrous dysplasia (FD) is a rare, benign bone developmental disorder that predominantly affects adolescents and young adults. Cranial bones are rarely involved. The definitive treatment for craniofacial FD in adults is complete resection and reconstruction. We present the case of a 20-year-old female with a painless, gradually enlarging scalp swelling in the left frontoparietal region for 10 years. Clinical evaluation showed no neurological deficits or signs of intracranial hypertension. Imaging, including CT and MRI, indicated diploe hypertrophy and a benign large diploic space lesion without intracranial complications. She underwent a craniectomy for mass removal with cranioplasty. Histopathological examination confirmed the diagnosis of FD. The outcome was favorable, with no recurrence at the one-year follow-up. FD is a rare, benign bone disorder characterized by abnormal fibrous tissue replacing normal bone, resulting in weakness and an increased risk of fracture. It can affect various intracranial locations, including the skull bones, the skull base, and the paranasal sinuses. Lesions in the cranial vault may result in visible deformities or functional issues. Diagnosis is based on radiological and histopathological findings, with bone biopsy being the preferred test. Management is primarily conservative, but surgery is indicated for functional preservation and complication prevention.
骨纤维异常增殖症（FD）是一种罕见的良性骨发育障碍，主要影响青少年和年轻成年人。颅骨很少受累。成人颅面部FD的 definitive 治疗方法是完全切除并重建。我们报告一例20岁女性病例，其左额顶区头皮出现无痛性、逐渐增大的肿胀10年。临床评估未发现神经功能缺损或颅内高压迹象。包括CT和MRI在内的影像学检查显示板障增厚以及良性的大的板障间隙病变，无颅内并发症。她接受了颅骨切除术以切除肿块并进行颅骨成形术。组织病理学检查确诊为FD。结果良好，在一年的随访中无复发。FD是一种罕见的良性骨疾病，其特征是异常纤维组织取代正常骨，导致骨骼脆弱和骨折风险增加。它可影响颅内的各个部位，包括颅骨、颅底和鼻窦。颅顶病变可能导致可见的畸形或功能问题。诊断基于影像学和组织病理学检查结果，骨活检是首选检查。治疗主要是保守治疗，但为了保留功能和预防并发症，手术是必要的。
