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白细胞破碎性血管炎中的同形反应:一例病例报告及文献综述更新

Koebner phenomenon in leukocytoclastic vasculitis: A case report and an updated review of the literature.

作者信息

Kassam Farah, Nurmohamed Sabrina, Haber Richard M

机构信息

Faculty of Medicine, The University of British Columbia, Vancouver, BC, Canada.

Division of Dermatology, Department of Medicine, University of Calgary, Calgary, AB, Canada.

出版信息

SAGE Open Med Case Rep. 2019 May 16;7:2050313X19850353. doi: 10.1177/2050313X19850353. eCollection 2019.

Abstract

Leukocytoclastic vasculitis is the most common form of cutaneous vasculitis. It is a neutrophilic small vessel vasculitis resulting from the deposition of circulating immune complexes. Henoch-Schonlein purpura is a systemic type of leukocytoclastic vasculitis, characterized by immunoglobulin A-mediated blood vessel injury. We present a case of Henoch-Schonlein purpura in an adult female manifesting with a vasculitic rash with Koebner phenomenon.

摘要

白细胞破碎性血管炎是皮肤血管炎最常见的形式。它是一种由循环免疫复合物沉积导致的嗜中性粒细胞性小血管炎。过敏性紫癜是白细胞破碎性血管炎的一种全身性类型,其特征为免疫球蛋白A介导的血管损伤。我们报告一例成年女性过敏性紫癜病例,表现为具有同形反应的血管炎性皮疹。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e1c1/6537234/21d5735dc648/10.1177_2050313X19850353-fig1.jpg

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