Plut Domen, Gorjanc Tamara
Clinical Radiology Institute, University Medical Centre Ljubljana, Ljubljana, Slovenia.
Faculty of Medicine, University of Ljubljana, Ljubljana, Slovenia.
Acta Radiol Open. 2019 Jun 12;8(6):2058460119854173. doi: 10.1177/2058460119854173. eCollection 2019 Jun.
Intrahepatic congenital portosystemic venous shunts are rare vascular anomalies. We report a unique case of a neonate with an intrahepatic congenital portosystemic venous shunt with concurrent congenital duodenal web. Such association has not been previously reported to our knowledge. Interestingly, the shunt became apparent on the seventh day, after a delayed start of oral feeding due to the neonate's recovery from the duodenal web surgery. The shunt was small and the clinical symptomatology mild. No direct treatment was required. The laboratory and the ultrasound follow-up of the child noted a spontaneous resolution of the shunt by the age of six months.
肝内先天性门体静脉分流是罕见的血管异常。我们报告了一例独特的新生儿病例,该新生儿患有肝内先天性门体静脉分流并伴有先天性十二指肠蹼。据我们所知,此前尚未有这种关联的报道。有趣的是,由于新生儿从十二指肠蹼手术中恢复,经口喂养开始延迟,分流在第七天变得明显。分流较小,临床症状轻微。无需直接治疗。对该患儿的实验室检查和超声随访发现,分流在六个月大时自行消退。