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本文引用的文献

1
Aquaporin-4 antibody titration in NMO patients treated with rituximab: A retrospective study.利妥昔单抗治疗的视神经脊髓炎患者中水通道蛋白4抗体滴定:一项回顾性研究。
Neurol Neuroimmunol Neuroinflamm. 2016 Dec 15;4(2):e317. doi: 10.1212/NXI.0000000000000317. eCollection 2017 Mar.
2
International consensus diagnostic criteria for neuromyelitis optica spectrum disorders.视神经脊髓炎谱系障碍国际共识诊断标准
Neurology. 2015 Jul 14;85(2):177-89. doi: 10.1212/WNL.0000000000001729. Epub 2015 Jun 19.
3
The spectrum of neuromyelitis optica (NMO) in childhood.儿童视神经脊髓炎(NMO)的谱系
J Child Neurol. 2012 Nov;27(11):1437-47. doi: 10.1177/0883073812451495. Epub 2012 Aug 1.
4
Evaluation of a multiparametric immunofluorescence assay for standardization of neuromyelitis optica serology.评估一种用于视神经脊髓炎血清学标准化的多参数免疫荧光分析方法。
PLoS One. 2012;7(6):e38896. doi: 10.1371/journal.pone.0038896. Epub 2012 Jun 12.
5
Contrasting disease patterns in seropositive and seronegative neuromyelitis optica: A multicentre study of 175 patients.视神经脊髓炎谱系疾病患者血清学阳性与血清学阴性患者的疾病特征对比:一项包含 175 例患者的多中心研究。
J Neuroinflammation. 2012 Jan 19;9:14. doi: 10.1186/1742-2094-9-14.
6
[Clinical features of Japanese pediatric patients with anti-aquaporin 4 antibody].
No To Hattatsu. 2011 Sep;43(5):359-65.
7
A benign form of neuromyelitis optica: does it exist?视神经脊髓炎的一种良性形式:它存在吗?
Arch Neurol. 2011 Jul;68(7):918-24. doi: 10.1001/archneurol.2011.127.
8
Intractable vomiting as the initial presentation of neuromyelitis optica.以难治性呕吐为首发表现的视神经脊髓炎。
Ann Neurol. 2010 Nov;68(5):757-61. doi: 10.1002/ana.22121.
9
Long-term follow-up of neuromyelitis optica with a pediatric onset.儿童起病的视神经脊髓炎的长期随访。
Neurology. 2010 Sep 21;75(12):1084-8. doi: 10.1212/WNL.0b013e3181f39a66.
10
CNS aquaporin-4 autoimmunity in children.儿童中枢神经系统水通道蛋白4自身免疫病
Neurology. 2008 Jul 8;71(2):93-100. doi: 10.1212/01.wnl.0000314832.24682.c6. Epub 2008 May 28.

一名患有视神经脊髓炎谱系障碍的13岁男孩视力的自发改善

Spontaneous Improvement of Visual Acuity in a 13-Year-Old Boy with Neuromyelitis Optica Spectrum Disorder.

作者信息

Yamaguchi Keiko, Hayashi Takaaki, Kiriyama Akiko, Iida Kie, Yoshimine Shoyo, Masuda Yoichiro, Shikishima Keigo, Ariizumi Mitsuko, Takahashi Genichiro, Nakano Tadashi

机构信息

Department of Ophthalmology, Katsushika Medical Center, The Jikei University School of Medicine, Tokyo, Japan.

Department of Ophthalmology, The Jikei University School of Medicine, Tokyo, Japan.

出版信息

Neuroophthalmology. 2018 Oct 29;43(2):114-119. doi: 10.1080/01658107.2018.1483951. eCollection 2019 Apr.

DOI:10.1080/01658107.2018.1483951
PMID:31312236
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC6619997/
Abstract

Ophthalmic and MRI evaluations of a 13-year-old boy who reported loss of visual acuity in his right eye demonstrated the presence of unilateral optic neuritis. After serological tests showed positivity for anti-aquaporin 4 antibody, he was diagnosed with neuromyelitis optica spectrum disorder. Encephalopathy and myelitis were not observed. Since his unilateral optic neuritis was considered to reflect mild disease activity, only follow-up observations were performed. Visual acuity and central scotoma improved 1 week after the first examination. In the absence of any specific treatments, good visual acuity has remained for 20 months, with no relapse of optic neuritis.

摘要

一名13岁男孩报告右眼视力丧失,眼科和MRI检查显示存在单侧视神经炎。血清学检查显示抗水通道蛋白4抗体呈阳性后,他被诊断为视神经脊髓炎谱系障碍。未观察到脑病和脊髓炎。由于认为他的单侧视神经炎反映了轻度疾病活动,因此仅进行了随访观察。首次检查1周后视力和中心暗点有所改善。在没有任何特异性治疗的情况下,良好的视力已维持20个月,视神经炎未复发。