Li Liubing, Wang Ying, Zhu Zhenhua, Zhou Jupu, Li Shuyuan, Qin Jianzhong
Department of Orthopaedics.
Department of General Surgery.
Medicine (Baltimore). 2019 Jul;98(29):e16367. doi: 10.1097/MD.0000000000016367.
Kashin-Beck disease (KBD) is known for some typical characters like finger joint enlargement, shortened fingers, and dwarfism. However, Avascular necrosis (AVN) of the talus in KBD has rarely been reported in the literature. Here, we reported on a KBD patient presented with partial AVN of the talus in conjunction with ankle and subtalar arthritis.
A 50-year-old woman presented with severe pain and limited range of motion in her left ankle and subtalar joint while walking for 2 years. She had been walking with the aid of crutches for many years. Conservative treatment with rigid orthosis and activity restriction could not help reduce the pain in the left foot.
Radiographs demonstrated that partial AVN was developed in the body of the talus and arthritis was viewed in the left ankle and subtalar joint. Hence, we established the diagnosis of partial talar AVN in conjunction with ankle and subtalar arthritis.
A conservative tibiotalocalcaneal fusion attempting to preserve as much viable talar body as possible was performed using a humeral locking plate and 2 cannulated compression screws.
Bone union proved by CT scan and a good alignment of the left limb were achieved at 4-month follow-up postoperatively.
Partial AVN of the talus along with ankle and subtalar arthritis in KBD patients has rarely been reported as it is not a common characteristic of KBD in clinical practice. Conservative tibiotalocalcaneal fusion could help preserving much more viable talar body, maintaining most structural integrity of the ankle joint, and achieving a stable and plantigrade foot postoperatively.
大骨节病(KBD)以一些典型特征而闻名,如手指关节肿大、手指缩短和侏儒症。然而,大骨节病距骨缺血性坏死(AVN)在文献中鲜有报道。在此,我们报告了一例大骨节病患者,其表现为距骨部分缺血性坏死并伴有踝关节和距下关节炎。
一名50岁女性,行走2年来左踝关节和距下关节出现严重疼痛且活动范围受限。她多年来一直借助拐杖行走。采用刚性矫形器和限制活动的保守治疗未能减轻左脚疼痛。
X线片显示距骨体出现部分缺血性坏死,左踝关节和距下关节存在关节炎。因此,我们诊断为距骨部分缺血性坏死合并踝关节和距下关节炎。
使用肱骨锁定钢板和2枚空心加压螺钉进行保守性胫距跟融合术,试图尽可能保留更多有活力的距骨体。
术后4个月随访时,CT扫描证实骨愈合,左下肢对线良好。
大骨节病患者距骨部分缺血性坏死合并踝关节和距下关节炎在临床实践中并非大骨节病的常见特征,因此鲜有报道。保守性胫距跟融合术有助于保留更多有活力的距骨体,维持踝关节的大部分结构完整性,并在术后实现稳定且足底着地的足部状态。