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类坏疽性脓皮病样钙化防御。

Calciphylaxis mimicking ecthyma gangrenosum.

作者信息

Tangkham Ranchana, Sangmala Siripan, Aiempanakit Kumpol, Chiratikarnwong Kanokphorn, Auepemkiate Sauvarat

机构信息

Department of Family Medicine and Preventive Medicine, Faculty of Medicine, Prince of Songkla University, Hat Yai, 90110 Songkhla, Thailand.

Division of Dermatology, Department of Internal Medicine, Faculty of Medicine, Prince of Songkla University, Hat Yai, Songkhla, Thailand.

出版信息

IDCases. 2019 Jul 11;18:e00594. doi: 10.1016/j.idcr.2019.e00594. eCollection 2019.

DOI:10.1016/j.idcr.2019.e00594
PMID:31360636
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC6639653/
Abstract

Calciphylaxis is a rare cutaneous disease that may cause fatal complications in patients on long-term dialysis. Early diagnosis and proper management decrease complications. However, it can mimic cutaneous infections, especially ecthyma gangrenosum and cutaneous vasculitis. The authors report on a patient with chronic kidney disease (CKD) on dialysis for 10 years who developed painful skin necrosis on his right thigh. The tissue culture was positive for , but the histopathology was compatible with calciphylaxis. This report aims to further the knowledge of physicians in order to help them recognize calciphylaxis in CKD patients with painful necrotic ulcers.

摘要

钙过敏症是一种罕见的皮肤疾病,可能会在长期透析的患者中引发致命并发症。早期诊断和恰当处理可减少并发症。然而,它可能会与皮肤感染相似,尤其是坏疽性脓皮病和皮肤血管炎。作者报告了一名患有慢性肾脏病(CKD)且已透析10年的患者,其右大腿出现了疼痛性皮肤坏死。组织培养结果为阳性,但组织病理学结果与钙过敏症相符。本报告旨在增进医生的认识,以帮助他们识别患有疼痛性坏死性溃疡的CKD患者中的钙过敏症。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8bbf/6639653/772f858106ea/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8bbf/6639653/3d4ff9f5d1be/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8bbf/6639653/2d34ef23bea9/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8bbf/6639653/772f858106ea/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8bbf/6639653/3d4ff9f5d1be/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8bbf/6639653/2d34ef23bea9/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8bbf/6639653/772f858106ea/gr3.jpg

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1
Calciphylaxis mimicking ecthyma gangrenosum.类坏疽性脓皮病样钙化防御。
IDCases. 2019 Jul 11;18:e00594. doi: 10.1016/j.idcr.2019.e00594. eCollection 2019.
2
Ecthyma gangrenosum: a rare cutaneous manifestation of a potentially fatal disease.坏疽性脓皮病:一种潜在致命疾病的罕见皮肤表现。
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Fulminant and relentless cutaneous necrosis with excruciating pain caused by calciphylaxis developing in a patient undergoing peritoneal dialysis.一名正在接受腹膜透析的患者发生钙化防御,出现暴发性且持续的皮肤坏死,并伴有剧痛。
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Ecthyma gangrenosum without bacteraemia in a leukaemic patient.一名白血病患者出现无菌血症的坏疽性脓皮病。
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引用本文的文献

1
Sodium Thiosulfate for Calciphylaxis Treatment in Patients on Peritoneal Dialysis: A Systematic Review.硫代硫酸钠治疗腹膜透析患者钙化防御:系统评价。
Medicina (Kaunas). 2023 Jul 14;59(7):1306. doi: 10.3390/medicina59071306.

本文引用的文献

1
Chronic Kidney Disease and Calciphylaxis: A Literature Review.慢性肾脏病与钙化防御:文献综述
Cureus. 2018 Sep 19;10(9):e3334. doi: 10.7759/cureus.3334.
2
Calciphylaxis.钙过敏症
N Engl J Med. 2018 May 3;378(18):1704-1714. doi: 10.1056/NEJMra1505292.
3
Clinical characteristics and risk factors associated with mortality in calcific uremic arteriolopathy.钙化性尿毒症小动脉病的临床特征及与死亡率相关的危险因素。
Int Urol Nephrol. 2017 Dec;49(12):2247-2256. doi: 10.1007/s11255-017-1721-9. Epub 2017 Oct 20.
4
Lack of evidence does not justify neglect: how can we address unmet medical needs in calciphylaxis?缺乏证据并不意味着可以忽视:我们如何解决钙化防御中未满足的医疗需求?
Nephrol Dial Transplant. 2016 Aug;31(8):1211-9. doi: 10.1093/ndt/gfw025. Epub 2016 Mar 22.
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Calciphylaxis: a systematic review of existing and emerging therapies.钙化防御:现有和新兴疗法的系统评价。
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Dermatological disease in patients with CKD.
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Calciphylaxis: natural history, risk factor analysis, and outcome.钙过敏症:自然病史、危险因素分析及预后
J Am Acad Dermatol. 2007 Apr;56(4):569-79. doi: 10.1016/j.jaad.2006.08.065. Epub 2006 Dec 1.
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An experimental model of "dermatomyositis" induced by calciphylaxis.由钙质沉着引起的“皮肌炎”实验模型。
Can Med Assoc J. 1961 Sep 30;85(14):770-6.
9
Calciphylaxis presenting with calf pain and plaques in four continuous ambulatory peritoneal dialysis patients and in one predialysis patient.四名持续非卧床腹膜透析患者及一名透析前患者出现伴有小腿疼痛和斑块的钙过敏。
Am J Kidney Dis. 1995 Mar;25(3):498-502. doi: 10.1016/0272-6386(95)90116-7.