Batista Kátia Tôrres, Martins Valney Claudino Sampaio, Schwartzman Ulises Prieto Y, Ferreira Telma Leonel
Rede Sarah de Hospitais de Reabilitação, Brasília, DF, Brasil.
Rev Bras Ortop (Sao Paulo). 2019 May;54(3):353-356. doi: 10.1016/j.rbo.2017.08.003. Epub 2019 Apr 16.
Myxofibrosarcoma is a rare soft tissue sarcoma. The authors present a case report regarding the excision and reconstruction of an extensive low-grade myxofibrosarcoma in the forearm, in the wrist, and in the hand of a young woman. A large-scale monobloc excision was performed according to resonance magnetic imaging (MRI) and transoperative histopathologic study findings. A dermal matrix and total skin graft associated with a postoperative physiotherapy program were used. The aspects related to the differential diagnosis of myxofibrosarcoma in a young patient, its infiltrative character, the extensive excision, the reconstruction in two surgical times (using a dermal matrix and a full-thickness skin graft), and the postoperative physical therapy program were considered important.
黏液纤维肉瘤是一种罕见的软组织肉瘤。作者报告了一例年轻女性前臂、腕部和手部广泛低度黏液纤维肉瘤的切除与重建病例。根据磁共振成像（MRI）和术中组织病理学研究结果进行了大规模整块切除。采用了真皮基质和全厚皮片移植，并结合术后物理治疗方案。年轻患者黏液纤维肉瘤的鉴别诊断、其浸润性特征、广泛切除、分两期进行重建（使用真皮基质和全厚皮片）以及术后物理治疗方案等方面被认为很重要。
