Bloch G, Menu P, Cachera J P, Tamari W, Mesnildrey P, Ichou J, Casasoprana A, Magnier S, Aubry P, Heurtematte Y
Service de chirurgie cardiaque, Hôpital Henri-Mondor, Créteil.
Arch Mal Coeur Vaiss. 1988 May;81(5):635-41.
The authors report their experience of surgery for subvalvular aortic obstruction in 82 patients aged from 4 to 44 years (mean 15 years). Nearly one-half of the patients presented with symptoms; the others were operated upon for various reasons: gradient exceeding 60 mmHg, development or aggravation of aortic regurgitation, positive exercise test, electrocardiographic or echocardiographic signs of left ventricular repercussions. Nineteen children had previously undergone surgery for another malformation, but the subvalvular aortic obstruction had either been missed during this first operation or had developed subsequently. The diaphragmatic pattern was the most frequent (62 cases); the fibromuscular pattern was less common (9 cases) and the tunnel pattern (6 cases) was regularly associated in this series with hypoplasia of the aortic ring. Obstruction due to faulty insertion of the mitral valve was encountered on 3 occasions. The operative technique for each anatomical pattern is described. Tunnel obstructions did not require primary aortoventriculoplasty without prosthetic valve replacement of apicoaortic conduits. In addition to treatment of associated lesions (including 4 cases of ventricular septal defect), 9 aortic commissurotomies, 6 aortic valvuloplasties and 4 aortic valve replacements were performed. The transaortic gradient was dramatically improved. The aortic regurgitation murmur subsided with or, usually, without valvuloplasty.(ABSTRACT TRUNCATED AT 250 WORDS)
作者报告了他们对82例年龄在4至44岁(平均15岁)的主动脉瓣下狭窄患者进行手术的经验。近一半患者有症状;其他患者因各种原因接受手术:压力阶差超过60 mmHg、主动脉瓣关闭不全的发生或加重、运动试验阳性、左心室受累的心电图或超声心动图表现。19名儿童此前因其他畸形接受过手术,但在首次手术中要么漏诊了主动脉瓣下狭窄,要么随后才出现。膈膜型最为常见(62例);纤维肌型较少见(9例),而在本系列中隧道型(6例)常伴有主动脉环发育不全。有3例因二尖瓣附着异常导致梗阻。描述了每种解剖类型的手术技术。隧道型梗阻无需在不置换人工瓣膜或行心尖主动脉管道的情况下进行一期主动脉心室成形术。除了治疗相关病变(包括4例室间隔缺损)外,还进行了9次主动脉瓣交界切开术、6次主动脉瓣成形术和4次主动脉瓣置换术。经主动脉压力阶差显著改善。主动脉瓣关闭不全杂音在有或通常无瓣膜成形术的情况下减轻。(摘要截短至250字)