Choi Jae Won, Choi Jun Young, Go Kyung Hyuk, Cheon Yun Hong, Kim Jong Woo, Lee Chung Eun, Park Hyun Oh
Department of Thoracic and Cardiovascular Surgery, Gyeongsang National University Hospital, Gyeongsang National University College of Medicine, Jinju, Korea.
Department of Pathology, Gyeongsang National University Hospital, Gyeongsang National University College of Medicine, Jinju, Korea.
Korean J Thorac Cardiovasc Surg. 2019 Aug;52(4):239-242. doi: 10.5090/kjtcs.2019.52.4.239. Epub 2019 Aug 5.
Noninfectious aortitis, inflammatory abdominal periaortitis, and idiopathic retroperitoneal fibrosis are chronic inflammatory diseases with unclear causes. Recent studies have shown that some cases of aortitis are associated with immunoglobulin G4 (IgG4)-related systemic disease. Herein, we report a case of IgG4-related aortitis (IgG4-RA) that was diagnosed after surgery. Our patient was a 46-year-old man who had experienced abdominal pain for several weeks. Preoperative evaluations revealed an area of aortitis on the infrarenal aorta. He underwent surgery, and histological examination resulted in a diagnosis of IgG4-RA.
非感染性主动脉炎、炎性腹部主动脉周围炎和特发性腹膜后纤维化是病因不明的慢性炎症性疾病。最近的研究表明,某些主动脉炎病例与免疫球蛋白G4(IgG4)相关的全身性疾病有关。在此,我们报告一例术后诊断为IgG4相关主动脉炎(IgG4-RA)的病例。我们的患者是一名46岁男性,数周来一直腹痛。术前评估显示肾下腹主动脉存在主动脉炎区域。他接受了手术,组织学检查确诊为IgG4-RA。