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儿童期起病的系统性红斑狼疮合并脑膜炎球菌败血症相关的急性石化心肌:1例死亡病例。

Acute petrified myocardium associated with meningococcal sepsis in childhood-onset systemic lupus erythematous: a fatal case.

作者信息

Santos Ana Carolina Etrusco Zaroni, Luglio Michele, Delgado Artur Figueiredo, Schuwartz Constance Dell Santo Vieira, Marques Heloísa Helena Sousa, Valões Clarissa Carvalho de Miranda, Dominguez Maria Andreina Cabrera, Carvalho Werther Brunow de, Silva Clovis Artur, Duarte-Neto Amaro Nunes

机构信息

Universidade de São Paulo, Hospital das Clínicas, Instituto da Criança, Unidade de Terapia Intensiva Pediátrica, São Paulo, São Paulo, Brazil.

Universidade de São Paulo, Hospital das Clínicas, Instituto da Criança, Departamento de Infectologia Pediátrica, São Paulo, São Paulo, Brazil.

出版信息

Rev Inst Med Trop Sao Paulo. 2019 Aug 8;61:e39. doi: 10.1590/S1678-9946201961039.

Abstract

Acute petrified myocardium associated with septic shock, diagnosed by autopsy has rarely been described. A 15-year-old adolescent male was diagnosed with childhood-onset systemic lupus erythematosus. One year later, he was hospitalized with fever, myalgia, headache, arthritis, vomiting, dyspnea and was diagnosed with sepsis secondary to bronchopneumonia and meningitis. Blood culture identified Neisseria meningitidis serogroup Y. Despite antibiotics and intensive therapeutic measures, he died after 29 days of hospitalization. The autopsy revealed necrotic cardiomyocytes with dystrophic calcification and interstitial fibrosis.

摘要

通过尸检诊断出的与感染性休克相关的急性石化心肌很少被描述。一名15岁的青少年男性被诊断为儿童期发病的系统性红斑狼疮。一年后,他因发热、肌痛、头痛、关节炎、呕吐、呼吸困难住院,被诊断为支气管肺炎和脑膜炎继发的败血症。血培养鉴定出Y群脑膜炎奈瑟菌。尽管采取了抗生素和强化治疗措施,但他在住院29天后死亡。尸检显示心肌细胞坏死,伴有营养不良性钙化和间质纤维化。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4b38/6690576/19b4ebf559f6/1678-9946-rimtsp-61-S1678-9946201961039-gf01.jpg

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