Yagnik Vipul D, Dawka Sushil
Department of Surgical Gastroenterology, Nishtha surgical hospital and research center, Patan, Gujarat, India.
Department of surgery, SSR Medical College, Belle Rive, Mauritius.
Clin Exp Gastroenterol. 2019 Jun 25;12:279-285. doi: 10.2147/CEG.S203697. eCollection 2019.
Extraskeletal Ewing's sarcoma (E-EWS)/peripheral primitive neuroectodermal tumor (pPNET) is a rare soft tissue tumor that arises from a multipotent progenitor cell and is considered to be of neuroectodermal origin. Although soft tissue E-EWS/pPNETs are common, they are exceedingly rare in the small bowel. Only 30 cases of E-EWS/pPNET of the small bowel have been reported. However, only one case of gastrointestinal perforation has been reported till today. Here, we report the second case of E- EWS/pPNET with gastrointestinal perforation.
骨外尤文肉瘤(E-EWS)/外周原始神经外胚层肿瘤(pPNET)是一种罕见的软组织肿瘤,起源于多能祖细胞,被认为是神经外胚层起源。虽然软组织E-EWS/pPNET很常见,但在小肠中极为罕见。小肠E-EWS/pPNET仅报道过30例。然而,迄今为止仅报道过1例胃肠道穿孔病例。在此,我们报告第二例伴有胃肠道穿孔的E-EWS/pPNET病例。