小肠原发性尤因肉瘤——一例报告并文献复习
Primary Ewing's sarcoma in a small intestine - a case report and review of the literature.
作者信息
Kolosov Andrej, Dulskas Audrius, Pauza Kastytis, Selichova Veslava, Seinin Dmitrij, Stratilatovas Eugenijus
机构信息
Vilnius University, Faculty of Medicine, Vilnius, Lithuania.
出版信息
BMC Surg. 2020 May 25;20(1):113. doi: 10.1186/s12893-020-00774-z.
BACKGROUND
Ewing's sarcoma usually presents in paediatric patients with its primary location being bone tissue. Nevertheless, we present such an adult case which arises from the small intestine. We registered thirty one cases of such origin published so far excluding ours.
CASE PRESENTATION
We report a case of 30 year old female who was admitted due to the persistent anaemia. Whole body computed tomography scan revealed abdominal mass in her left upper abdominal compartment. Surgery on the mass originating from jejunum was performed, although due to extremely complicated postoperative period and rapid dissemination no additional therapy had been performed. The tumour was positive for CD99, ERG, CD56, Synaptophysin, PanCK, Cam5.2.
CONCLUSION
Extraosseus Ewing's sarcoma is extremely rare entity, with poor prognosis.
背景
尤因肉瘤通常发生于儿童患者，主要位于骨组织。然而，我们在此呈现一例起源于小肠的成人病例。我们登记了迄今为止已发表的除我们的病例外的31例此类起源的病例。
病例报告
我们报告一例30岁女性，因持续性贫血入院。全身计算机断层扫描显示左上腹有腹部肿块。对起源于空肠的肿块进行了手术，尽管术后情况极其复杂且肿瘤迅速扩散，但未进行额外治疗。肿瘤CD99、ERG、CD56、突触素、全细胞角蛋白、Cam5.2呈阳性。
结论
骨外尤因肉瘤是一种极其罕见的疾病，预后较差。
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