Pandit Bhagya Narayan, Subramaniyan Siva, Kumar Tarun, Agrawal Richa, Vatsa Deepankar
Department of Cardiology, Guru Gobind Singh Indraprastha University, New Delhi, India.
Int J Angiol. 2019 Sep;28(3):202-206. doi: 10.1055/s-0038-1639591. Epub 2018 Mar 28.
Sinus of Valsalva aneurysm (SVA) is rare, and aneurysm of the left sinus of Valsalva is extremely rare cardiovascular disease. Clinical presentation can vary from mostly asymptomatic to catastrophic life-threatening emergency. We report four extremely rare cases of SVA with different manifestations of which one case involved left aortic sinus with large unruptured aneurysm causing severe mitral regurgitation (MR) and severe aortic regurgitation (AR). The second case aneurysm was from right sinus presented with trifascicular block with intermittent complete heart block (CHB). Third was a diagnosed case of unruptured right SVA and while awaiting for surgery he had sudden cardiac death (SCD) at home. Therefore, SVA can present from asymptomatic to life-threatening condition, such as SCD. To the best of our knowledge, there are individual case reports in literature, and this is the first case series of unruptured SVA in literature highlighting the rarity of this disease.
瓦氏窦瘤(SVA)较为罕见,而左瓦氏窦瘤更是极为罕见的心血管疾病。临床表现差异很大,从大多无症状到危及生命的灾难性急症都有。我们报告了4例极为罕见的SVA病例,表现各异,其中1例累及左主动脉窦,有巨大未破裂动脉瘤,导致严重二尖瓣反流(MR)和严重主动脉瓣反流(AR)。第2例动脉瘤起源于右窦,表现为三分支阻滞伴间歇性完全性心脏传导阻滞(CHB)。第3例为已确诊的未破裂右SVA病例,在等待手术期间在家中发生心源性猝死(SCD)。因此,SVA可表现为从无症状到危及生命的情况,如SCD。据我们所知,文献中有个别病例报告,而本文是文献中首个未破裂SVA病例系列,突出了该疾病的罕见性。