Successful Treatment of PAPA Syndrome with Dual Adalimumab and Tacrolimus Therapy.
作者信息
Sood Amika K, McShane Diana B, Googe Paul B, Wu Eveline Y
机构信息
Division of Pediatric Allergy, Immunology, and Rheumatology, University of North Carolina at Chapel Hill, Chapel Hill, NC, USA.
Department of Dermatology, University of North Carolina at Chapel Hill, Chapel Hill, NC, USA.
出版信息
J Clin Immunol. 2019 Nov;39(8):832-835. doi: 10.1007/s10875-019-00685-6. Epub 2019 Aug 30.
Abstract
摘要
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Dysregulated neutrophil responses and neutrophil extracellular trap formation and degradation in PAPA syndrome.PAPA 综合征中失调的中性粒细胞反应和中性粒细胞胞外诱捕网的形成与降解。
Ann Rheum Dis. 2018 Dec;77(12):1825-1833. doi: 10.1136/annrheumdis-2018-213746. Epub 2018 Aug 21.
2
Pyoderma gangrenosum in an infant: A case report and review of the literature.婴儿坏疽性脓皮病：一例病例报告及文献综述
Pediatr Dermatol. 2018 Sep;35(5):e257-e261. doi: 10.1111/pde.13471. Epub 2018 Apr 15.
3
PAPA, PASH and PAPASH Syndromes: Pathophysiology, Presentation and Treatment.PAPA、PASH和PAPASH综合征：病理生理学、临床表现及治疗
Am J Clin Dermatol. 2017 Aug;18(4):555-562. doi: 10.1007/s40257-017-0265-1.
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Autoinflammation in pyoderma gangrenosum and its syndromic form (pyoderma gangrenosum, acne and suppurative hidradenitis).坏疽性脓皮病及其综合征形式（坏疽性脓皮病、痤疮和化脓性汗腺炎）中的自身炎症。
Br J Dermatol. 2017 Jun;176(6):1588-1598. doi: 10.1111/bjd.15226. Epub 2017 Apr 16.
5
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Curr Opin Rheumatol. 2016 Sep;28(5):550-9. doi: 10.1097/BOR.0000000000000314.
6
Single amino acid charge switch defines clinically distinct proline-serine-threonine phosphatase-interacting protein 1 (PSTPIP1)-associated inflammatory diseases.单个氨基酸电荷转换定义了临床上不同的脯氨酸 - 丝氨酸 - 苏氨酸磷酸酶相互作用蛋白1（PSTPIP1）相关炎症性疾病。
J Allergy Clin Immunol. 2015 Nov;136(5):1337-45. doi: 10.1016/j.jaci.2015.04.016. Epub 2015 May 27.
7
Successful treatment of PASH syndrome with infliximab, cyclosporine and dapsone.成功使用英夫利昔单抗、环孢素和氨苯砜治疗 PAS 综合征。
J Eur Acad Dermatol Venereol. 2015 Nov;29(11):2243-7. doi: 10.1111/jdv.12765. Epub 2014 Oct 28.
8
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