Derbel B, Krarti N, Ghedira F, Ben Mrad M, Hedhli M, Ziadi J, Denguir R
Faculté de médecine de Tunis, université de Tunis El Manar, 1007 Tunis Tunisia; Service de chirurgie cardiovasculaire, hôpital La Rabta, 1007 Tunis Tunisia.
Service de chirurgie cardiovasculaire, hôpital La Rabta, 1007 Tunis Tunisia.
J Med Vasc. 2019 Sep;44(5):354-358. doi: 10.1016/j.jdmv.2019.06.005. Epub 2019 Aug 7.
Bilateral absence of the superior vena cava (SVC) is an uncommon congenital vascular anomaly, mainly asymptomatic, usually undetected, and often associated with other cardiac anomalies. Though usually harmless and totally innocent, this vascular anomaly might complicate cardiovascular surgery, the insertion of a central venous catheter and the transvenous placement of a pacemaker. This SVC anomaly is still not well known, underdiagnosed and its incidence is much higher than described. A better understanding of this anomaly and its detection could play a key role in avoiding its potential complications. We are sharing a case of a female adult, with no medical history, who presented herself to the department of visceral surgery with a collateral venous circulation of the upper thorax, that was at first, mistaken for a portal hypertension syndrome, findings were pushed to finally conclude a bilateral absence of the SVC.
双侧上腔静脉缺失是一种罕见的先天性血管异常，主要表现为无症状，通常未被发现，且常与其他心脏异常相关。尽管这种血管异常通常无害且完全无大碍，但可能会使心血管手术、中心静脉导管插入术和起搏器经静脉置入术变得复杂。这种上腔静脉异常仍未被充分了解，诊断不足，其发病率远高于所描述的情况。更好地了解这种异常及其检测方法对于避免其潜在并发症可能起着关键作用。我们分享一例成年女性病例，该患者无病史，因上胸部侧支静脉循环就诊于内脏外科，最初被误诊为门静脉高压综合征，最终经检查确诊为双侧上腔静脉缺失。
