丙酮酸脱氢酶（E1）缺乏的免疫化学证据。 - Suppr

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超能文献

Immunochemical evidence of pyruvate dehydrogenase (E1) deficiency.

作者信息

Kitano A, Akaboshi I, Endo F, Matsuda I, Okano Y, Hase Y, Nagao Y, Kamoshita S, Miyabayashi S, Narisawa K

机构信息

Department of Pediatrics, Kumamoto University Medical School, Japan.

出版信息

J Inherit Metab Dis. 1988;11(3):329-32. doi: 10.1007/BF01800386.

DOI:10.1007/BF01800386

PMID:3148083

Abstract

摘要

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Immunochemical evidence of pyruvate dehydrogenase (E1) deficiency.丙酮酸脱氢酶（E1）缺乏的免疫化学证据。

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引用本文的文献

Eur J Pediatr. 1990 Apr;149(7):487-92. doi: 10.1007/BF01959401.

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Purification and immunochemical studies of pyruvate dehydrogenase complex from rat heart, and cell-free synthesis of lipoamide dehydrogenase, a component of the complex.大鼠心脏丙酮酸脱氢酶复合体的纯化及免疫化学研究，以及该复合体成分之一硫辛酰胺脱氢酶的无细胞合成。

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Pyruvate dehydrogenase complex activity in normal and deficient fibroblasts.正常和成纤维细胞缺陷型中的丙酮酸脱氢酶复合物活性

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Cleavage of structural proteins during the assembly of the head of bacteriophage T4.在噬菌体T4头部组装过程中结构蛋白的切割

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Low immunogenicity of the common lipoamide dehydrogenase subunit (E3) of mammalian pyruvate dehydrogenase and 2-oxoglutarate dehydrogenase multienzyme complexes.哺乳动物丙酮酸脱氢酶和2-氧代戊二酸脱氢酶多酶复合物常见的硫辛酰胺脱氢酶亚基（E3）的低免疫原性。

Biochem J. 1985 Mar 1;226(2):509-17. doi: 10.1042/bj2260509.

Immunochemical analysis of normal and mutant forms of human pyruvate dehydrogenase.人丙酮酸脱氢酶正常形式和突变形式的免疫化学分析。

Biochem J. 1986 Oct 1;239(1):89-96. doi: 10.1042/bj2390089.

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J Biol Chem. 1987 May 25;262(15):7398-403.

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