Department of Pathology, University of Tennessee Health Sciences Center (UTHSC), Memphis.
Department of Radiology, Methodist University Hospital (MUH), Memphis; Memphis Veteran affairs medical center (VAMC), Memphis.
Pathol Res Pract. 2019 Oct;215(10):152549. doi: 10.1016/j.prp.2019.152549. Epub 2019 Aug 24.
Salivary duct carcinoma (SDC) is an aggressive malignancy, resembling high-grade ductal carcinoma of the breast. Histologically, it shows cords and nests with cribriforming, marked nuclear atypia, comedonecrosis, perineural, and lymphovascular invasion. We report a rare case of SDC in a 61-year-old woman presenting with facial asymmetry, dysphagia, and cervical lymphadenopathy. Imaging showed an ill-defined infiltrating mass in parotid gland and multiple enlarged cervical lymph nodes. Histologically, the largest focus of tumor consisted of an intra-parotid lymph node replaced by sheets of bland appearing oncocytic tumor cells with abundant cytoplasm, centrally placed nucleus, and single prominent nucleolus. No mitotic figures were identified and focal areas showed nests with comedonecrosis and desmoplastic stromal response. Tumor showed strong positive staining for androgen receptor, CK7 and GATA-3. In addition, tumor stained strong positive for Her2neu making the patient amenable to Herceptin. NGS detected mutation in HRAS (p.Q61R) and a novel, not previously reported mutation in PIK3CA, (exon 21, p.H1047L). This case represents a rare presentation of SDC with bland cellular morphology unlike the usual associated high grade features. In addition, it reemphasizes the importance of androgen receptor in differential diagnosis from its mimics like oncocytic carcinoma and oncocytic variant of mucoepidermoid carcinoma. Further, Her2neu immunohistochemical status can be used for diagnosis as well as guide targeted therapy in these aggressive tumors.
涎腺导管癌(SDC)是一种侵袭性恶性肿瘤,类似于乳腺的高级别导管癌。组织学上,它表现为有筛状结构的条索和巢状结构,具有显著的核异型性、粉刺样坏死、神经周围和血管淋巴管侵犯。我们报告了一例罕见的 61 岁女性 SDC 病例,表现为面部不对称、吞咽困难和颈部淋巴结病。影像学显示腮腺内边界不清的浸润性肿块和多个增大的颈部淋巴结。组织学上,肿瘤最大的焦点由一个被片状、外观温和的嗜酸细胞肿瘤细胞取代的腮腺内淋巴结组成,这些肿瘤细胞具有丰富的细胞质、中央位置的核和单个突出的核仁。未发现有丝分裂象,局灶区域可见巢状结构伴有粉刺样坏死和纤维母细胞性间质反应。肿瘤强烈表达雄激素受体、CK7 和 GATA-3。此外,肿瘤对 Her2neu 呈强阳性染色,使患者能够接受曲妥珠单抗治疗。NGS 检测到 HRAS(p.Q61R)突变和 PIK3CA 的一个新的、以前未报道的突变(exon 21,p.H1047L)。该病例代表了一种罕见的 SDC 表现,具有温和的细胞形态,与通常相关的高级别特征不同。此外,它再次强调了雄激素受体在鉴别诊断中的重要性,其可以与嗜酸细胞癌和黏液表皮样癌的嗜酸细胞变体等模拟物相区分。此外,Her2neu 免疫组化状态可用于诊断,并指导这些侵袭性肿瘤的靶向治疗。