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Successful Treatment of Glycine-Receptor-Antibody-Mediated Progressive Encephalomyelitis with Rigidity and Myoclonus by Combining Steroids and Azathioprine.

作者信息

Lee Eung Joon, Kim Kitae, Choi Jeong Yoon, Park Kyung Seok

机构信息

Department of Neurology, Seoul National University Hospital, Seoul National University College of Medicine, Seoul, Korea.

Department of Neurology, Seoul National University Bundang Hospital, Seoul National University College of Medicine, Seongnam, Korea.

出版信息

J Clin Neurol. 2019 Oct;15(4):581-582. doi: 10.3988/jcn.2019.15.4.581.

DOI:10.3988/jcn.2019.15.4.581
PMID:31591852
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC6785484/
Abstract
摘要

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引用本文的文献

1
Anti-glycine receptor antibody-positive progressive encephalomyelitis with rigidity and myoclonus initially presenting with one-sided stiff face: A case report.抗甘氨酸受体抗体阳性的僵人综合征合并肌阵挛性进行性脑脊髓炎,最初表现为单侧面部僵硬:病例报告
Front Neurol. 2022 Oct 26;13:1021437. doi: 10.3389/fneur.2022.1021437. eCollection 2022.

本文引用的文献

1
Redefining progressive encephalomyelitis with rigidity and myoclonus after the discovery of antibodies to glycine receptors.在发现抗甘氨酸受体抗体后对伴有强直和肌阵挛的进行性脑脊髓炎的重新定义。
Curr Opin Neurol. 2017 Jun;30(3):310-316. doi: 10.1097/WCO.0000000000000450.
2
Successful immune moderation treatment for progressive encephalomyelitis with rigidity and myoclonus.成功的免疫调节治疗用于伴强直和肌阵挛的进行性脑脊髓炎。
Intern Med. 2015;54(2):219-21. doi: 10.2169/internalmedicine.54.3760. Epub 2015 Jan 15.
3
Glycine receptor antibodies in PERM and related syndromes: characteristics, clinical features and outcomes.
PERM 及相关综合征中的甘氨酸受体抗体:特征、临床特征和结局。
Brain. 2014 Aug;137(Pt 8):2178-92. doi: 10.1093/brain/awu142. Epub 2014 Jun 20.
4
Anti-glycine receptor antibody mediated progressive encephalomyelitis with rigidity and myoclonus associated with breast cancer.抗甘氨酸受体抗体介导的伴有僵硬和肌阵挛的进行性脑脊髓炎,与乳腺癌相关。
Case Rep Neurol Med. 2013;2013:589154. doi: 10.1155/2013/589154. Epub 2013 Jul 10.
5
Glycine receptor antibody mediated Progressive Encephalomyelitis with Rigidity and Myoclonus (PERM): a rare but treatable neurological syndrome.甘氨酸受体抗体介导的僵人综合征伴进行性脑脊髓炎(PERM):一种罕见但可治疗的神经综合征。
Pract Neurol. 2014 Apr;14(2):123-7. doi: 10.1136/practneurol-2013-000511. Epub 2013 Apr 5.
6
Stiff-man syndrome and variants: clinical course, treatments, and outcomes.僵人综合征及其变异型:临床病程、治疗方法及预后
Arch Neurol. 2012 Feb;69(2):230-8. doi: 10.1001/archneurol.2011.991.
7
Glycine receptor antibodies are detected in progressive encephalomyelitis with rigidity and myoclonus (PERM) but not in saccadic oscillations.甘氨酸受体抗体在进行性肌阵挛性脑脊髓炎伴僵硬和肌阵挛(PERM)中被检测到,但不在扫视性眼球震颤中被检测到。
J Neurol. 2012 Aug;259(8):1566-73. doi: 10.1007/s00415-011-6377-2. Epub 2012 Jan 4.
8
Progressive encephalomyelitis, rigidity, and myoclonus: a novel glycine receptor antibody.进行性脑脊髓炎、强直和肌阵挛:一种新型甘氨酸受体抗体
Neurology. 2008 Oct 14;71(16):1291-2. doi: 10.1212/01.wnl.0000327606.50322.f0.
9
The stiff man and stiff man plus syndromes.僵人综合征及僵人叠加综合征
J Neurol. 1999 Aug;246(8):648-52. doi: 10.1007/s004150050425.
10
Progressive encephalomyelitis with rigidity.进行性脑脊髓炎伴强直
Brain. 1976 Mar;99(1):27-42. doi: 10.1093/brain/99.1.27.