Hatami Mohammadmehdi, Doozandeh Azadeh, Feizi Mohadeseh
Ophthalmic Research Center, Shahid Beheshti University of Medical Sciences, Tehran, Iran.
J Ophthalmic Vis Res. 2019 Jul 18;14(3):370-375. doi: 10.18502/jovr.v14i3.4793. eCollection 2019 Jul-Sep.
To report a case of advanced childhood glaucoma secondary to congenital ectropion uveae (CEU).
The patient was a seven-year-old boy with unilateral glaucoma secondary to CEU and facial asymmetry, mild unilateral ptosis, and proptosis in the left eye. The intraocular pressure (IOP) was 28 mmHg and cup-to-disc ratio was 0.8 in the left eye. After starting glaucoma medication, IOP decreased to 21 mmHg. In view of the uncontrolled IOP with medication and high cup-to-disc ratio and increased axial length of the left eye, mitomycin-C (MMC)-augmented trabeculectomy was planned. Despite sub-tenon MMC injection and bleb needling, the bleb failed after six months, and we had to perform a shunt procedure to control the IOP.
Although CEU is rare, ophthalmologists should be familiar with this syndrome because of the high frequency of glaucoma and its challenging management during childhood.
报告一例继发于先天性葡萄膜外翻（CEU）的晚期儿童青光眼病例。
该患者为一名7岁男孩，患有继发于CEU的单侧青光眼，伴有面部不对称、轻度单侧上睑下垂和左眼眼球突出。左眼眼压（IOP）为28 mmHg，杯盘比为0.8。开始使用青光眼药物治疗后，眼压降至21 mmHg。鉴于药物治疗无法控制眼压、杯盘比高以及左眼眼轴长度增加，计划行丝裂霉素C（MMC）辅助小梁切除术。尽管进行了球结膜下MMC注射和滤泡针刺，但6个月后滤泡仍失败，我们不得不进行分流手术以控制眼压。
尽管CEU罕见，但由于青光眼发病率高且儿童期治疗具有挑战性，眼科医生应熟悉这种综合征。
