Dowling J L, Albert D M, Nelson L B, Walton D S
Ophthalmology. 1985 Jul;92(7):912-21. doi: 10.1016/s0161-6420(85)33935-0.
We present nine patients with unilateral congenital ectropion uveae (hyperplasia of the iris pigment border), iris hypoplasia, characteristic gonioscopic findings, and glaucoma. A majority of these patients also demonstrated mild ptosis. In none of these patients were there any associated systemic abnormalities. The apparent ectropion uveae results from spread of the iris pigment epithelium beyond the iris ruff and onto the anterior surface of the iris. In two patients with this abnormality, histopathologic and electron microscopic findings are presented. All patients with congenital ectropion uveae should be carefully examined periodically to detect glaucoma.
我们报告了9例患有单侧先天性虹膜外翻（虹膜色素边界增生）、虹膜发育不全、特征性前房角镜检查结果及青光眼的患者。这些患者中的大多数还表现出轻度上睑下垂。这些患者均未伴有任何全身性异常。明显的虹膜外翻是由于虹膜色素上皮扩散至虹膜卷边之外并延伸到虹膜前表面所致。本文展示了2例患有此异常的患者的组织病理学和电子显微镜检查结果。所有先天性虹膜外翻患者均应定期接受仔细检查以检测青光眼。
